Orbital manifestation of whipple's disease: An atypical case

被引：10

作者：

Lieger, Olivier ^{[1
]}

Otto, Sven ^{[1
]}

Clemetson, Isabelle Ann ^{[1
]}

Arnold, Marlene ^{[1
]}

Iizuka, Tateyuki ^{[1
]}

机构：

[1] Univ Bern, Dept Cranio Maxillofacial Surg, CH-3012 Bern, Switzerland

来源：

JOURNAL OF CRANIO-MAXILLOFACIAL SURGERY | 2007年 / 35卷 / 08期

关键词：

whipple disease; exophthalmos; orbit; inflammatory pseudotumour of orbit; surgery;

D O I：

10.1016/j.jcms.2007.03.005

中图分类号：

R78 [口腔科学];

学科分类号：

1003 ;

摘要：

Background: Whipple's disease is a systemic disorder caused by an infection with a gram-positive bacillus, Tropheryma whipplei. Almost every organ system can be affected in Whipple's disease, resulting in varying clinical symptoms. Case report: As far as we are aware, this report of a 61-year-old male is the first presenting with a periorbital manifestation of the disease, with severe exophthalmos and optic nerve involvement, leading to rapid visual loss. This emergency case was successfully treated by a surgical orbital decompression combined with systemic use of antibiotics and steroids. Conclusion: Whipple's disease can affect the periorbital tissues and the optic nerve, causing massive exophthalmos and serious transient visual loss. In such a case surgical decompression of the affected orbit combined with antibiotics and steroids is a recommended valid treatment option. (c) 2007 European Association for Cranio-Maxillofacial Surgery.

引用

页码：393 / 396

页数：4

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