Overview of Progressive Familial Intrahepatic Cholestasis

被引：21

作者：

Hassan, Sara ^{[1
]}

Hertel, Paula ^{[2
]}

机构：

[1] Mayo Clin, Div Gastroenterol Hepatol & Nutr, Dept Pediat, 200 First St Southwest, Rochester, MN 55905 USA

[2] Texas Childrens Hosp, Baylor Coll Med, Dept Pediat, Div Gastroenterol Hepatol & Nutr, 6621 Fannin St, Houston, TX 77030 USA

来源：

CLINICS IN LIVER DISEASE | 2022年 / 26卷 / 03期

关键词：

PFIC; Cholestasis; FIC1; BSEP; MDR3; TJP2; MYO5B; FXR; USP53; SALT EXPORT PUMP; LIVER-TRANSPLANTATION; BILIARY DIVERSION; HEPATOCELLULAR-CARCINOMA; MOLECULAR-MECHANISMS; URSODEOXYCHOLIC ACID; MUTATIONS; DISEASE; VARIANTS; CHILDREN;

D O I：

10.1016/j.cld.2022.03.003

中图分类号：

R57 [消化系及腹部疾病];

学科分类号：

摘要：

[No abstract available]

引用

页码：371 / 390

页数：20

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