The Heart Muscle and Valve Involvement in Marfan Syndrome, Loeys-Dietz Syndromes, and Collagenopathies

被引:10
|
作者
Fusco, Adelaide [1 ]
Mauriello, Alfredo [1 ]
Lioncino, Michele [1 ]
Palmiero, Giuseppe [1 ]
Fratta, Fiorella [1 ]
Granato, Chiara [2 ]
Cirillo, Annapaola [1 ]
Caiazza, Martina [1 ]
Monda, Emanuele [1 ]
Credendino, Antonello [3 ]
Signore, Giovanni [1 ]
Natale, Francesco [1 ]
Chiosi, Flavia [4 ]
Scarano, Gioacchino [1 ]
Della Corte, Alessandro [1 ]
Nistri, Stefano [5 ]
Russo, Maria Giovanna [1 ]
Limongelli, Giuseppe [1 ]
Pepe, Guglielmina [6 ]
机构
[1] Univ Campania Luigi Vanvitelli, Dept Translat Med Sci, I-80131 Naples, Italy
[2] Vall dHebron Inst Recerca VHIR, Grp Enfermedades Cardiovasc, Barcelona, Spain
[3] Monaldi Hosp, Dept Orthopaed, AORN Colli, Naples, Italy
[4] Azienda Osped Colli AORN Monaldi, Dept Ophthalmol, I-80100 Naples, Italy
[5] CMSR Veneto Med, Cardiol Serv, Altavilla Vicentina, Italy
[6] Univ Florence, CRR Tuscany Marfan Ctr, Dept Expt & Clin Med, Florence, Italy
关键词
Marfan syndrome; Ehlers-Danlos syndrome; Loeys-Dietz syndrome; Fibrillinopathies; Collagenophaties; TGFbetapathies; Cardiomyopathy: mitral valve prolapse; BICUSPID AORTIC-VALVE; EHLERS-DANLOS-SYNDROME; CARDIOVASCULAR MANIFESTATIONS; FBN1; MUTATIONS; DISSECTION; ANEURYSM; PROLAPSE; ASSOCIATION; MANAGEMENT; PHENOTYPES;
D O I
10.1016/j.hfc.2021.07.007
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
[No abstract available]
引用
收藏
页码:165 / 175
页数:11
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