Double lung transplantation for end-stage Kartagener syndrome: a case report and literature review

被引：13

作者：

Wang, Bo ^{[1
]}

Zhang, Xinghua ^{[1
]}

Jiang, Wenyang ^{[1
]}

Huang, Jie ^{[1
]}

Chen, Jingyu ^{[2
]}

Kreisel, Daniel ^{[3
]}

Danguilan, Jose Luis J. ^{[4
]}

Hsin, Michael ^{[5
]}

Lin, Huiqing ^{[1
]}

机构：

[1] Wuhan Univ, Renmin Hosp, Dept Thorac Surg, Wuhan 430060, Peoples R China

[2] Nanjing Med Univ, Affiliated Wuxi Peoples Hosp, Dept Thorac Surg, Wuxi 214000, Jiangsu, Peoples R China

[3] Washington Univ, Div Cardiothorac Surg, St Louis, MO USA

[4] Lung Ctr Philippines, Dept Thorac Surg & Anesthesia, Quezon City, Philippines

[5] Queen Mary Hosp, Dept Cardiothorac Surg, Hong Kong, Peoples R China

来源：

JOURNAL OF THORACIC DISEASE | 2020年 / 12卷 / 04期

基金：

中国国家自然科学基金;

关键词：

Kartagener syndrome; lung transplantation; primary ciliary dyskinesia; situs inversus; PRIMARY CILIARY DYSKINESIA; SITUS-INVERSUS; OUTCOMES;

D O I：

10.21037/jtd.2020.02.28

中图分类号：

R56 [呼吸系及胸部疾病];

学科分类号：

摘要：

Kartagener syndrome (KS) is an autosomal recessive disorder characterized by situs inversus, paranasal sinusitis and bronchiectasis. We report the successful use of double lung transplant (DLTx) to treat end-stage KS. A 49-year-old Han woman was admitted to Renmin Hospital (Wuhan University, China) in September 2017 with a >= 15 year history of chronic productive cough that had worsened during the past year. Clinical examination and imaging investigations revealed respiratory failure and situs inversus consistent with KS. The patient was successfully treated with DLTx involving bilateral bronchial anastomoses. DLTx is a feasible treatment option for end-stage KS.

引用

页码：1588 / 1594

页数：7

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