Primary antiphospholipid antibody syndrome and cardiac involvement in a child

被引:13
作者
Clauss, SB
Manco-Johnson, MJ
Quivers, E
Takemoto, C
Spevak, PJ [1 ]
机构
[1] Johns Hopkins Univ, Dept Pediat, Baltimore, MD 21287 USA
[2] Univ Colorado, Ctr Hlth Sci, Dept Pediat, Aurora, CO 80045 USA
[3] Childrens Hosp, Aurora, CO 80045 USA
[4] Childrens Natl Med Ctr, Dept Pediat, Washington, DC 20010 USA
关键词
antiphospholipid antibody syndrome; valve thrombosis;
D O I
10.1007/s00246-002-0273-6
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
We report a case of polyvalvar disease and recurrent thrombosis in a 2-year-old boy due to primary antiphospholipid antibody syndrome. His diagnosis was delayed, and he was treated for other diagnoses, including culture-negative endocarditis. Primary antiphospholipid antibody syndrome is rarely discussed in the pediatric cardiology literature, and this case highlights the need for early diagnosis to prevent recurrent valve dysfunction and thrombosis.
引用
收藏
页码:292 / 294
页数:3
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