Congenital epignathus associated with a cleft palate: a case report

被引：3

作者：

Mutombo, Fabrice Lele ^{[1
]}

Kikuhe, Jason Nzanzu ^{[2
]}

Mwanamolo, Noe Kasereka ^{[1
]}

Erickson, Marc H. ^{[3
]}

Wetzig, Neil ^{[1
]}

Kakule, Medard Kabuyaya ^{[1
,4
]}

机构：

[1] Heal Africa Hosp, Surg Dept, Goma, DEM REP CONGO

[2] GOMA Prov Referral Hosp, ENT Dept, Goma, DEM REP CONGO

[3] Ft Mem Hosp, Surg Dept, Milwaukee, WI USA

[4] Univ Goma, Surg Dept, Fac Med, Goma, DEM REP CONGO

来源：

JOURNAL OF MEDICAL CASE REPORTS | 2021年 / 15卷 / 01期

关键词：

Epignathus; Teratoma; Cleft palate; Airway obstruction; MANAGEMENT; TERATOMAS;

D O I：

10.1186/s13256-021-03007-w

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

BackgroundEpignathus is a rare, benign, congenital teratoma of the hard palate with an estimated incidence of 1 in 200,000 live births. Epignathus frequently leads to a high mortality (80-100%) due to airway obstruction in the neonatal period.Case presentationWe report a case of successful management of a rare oropharyngeal teratoma in a African newborn girl who was referred to our institute with a large protruding intraoral mass, combined with cleft palate, causing some respiratory compromise. The palatal mass was removed on the fifth day after birth, and a palatoplasty performed on day 30.ConclusionEpignathus is a life-threatening condition at the time of delivery. Appropriate management begins with securing the airway, followed by complete resection of the tumor.

引用

页数：4

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