Activation of the unfolded protein response (UPR) by ΔF508 CFTR and transcriptional suppression of CFTR expression by the UPR

被引:0
|
作者
Bartoszewski R. [1 ]
Rab A. [1 ,2 ]
Wakefield J. [3 ]
Bebok Z. [1 ,2 ]
机构
[1] Univ Alabama, Cell Biol, Birmingham, AL USA
[2] Univ Alabama, Gregory Fleming James Cyst Fibrosis Res Ctr, Birmingham, AL USA
[3] Tranzyme Inc, Birmingham, AL USA
关键词
D O I
暂无
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
引用
收藏
页码:214 / 214
页数:1
相关论文
共 50 条
  • [21] PROCESSING OF CFTRΔF508 IS SPECIES-SPECIFIC
    Ostedgaard, L. S.
    Vermeer, D.
    Karp, P.
    Zhang, Y.
    Rokhlina, T.
    Welsh, M. J.
    PEDIATRIC PULMONOLOGY, 2009, : 223 - 223
  • [22] RESTORATION OF ΔF508 CFTR TRAFFICKING BY FARNESYLATION INHIBITOR
    Yang, X.
    Gong, X.
    Zhang, R.
    Zaman, K.
    Frizzell, R. A.
    Sun, F.
    PEDIATRIC PULMONOLOGY, 2010, : 224 - 224
  • [23] 4-Chlorobenzo[F]isoquinoline (CBIQ), a novel activator of CFTR and ΔF508 CFTR
    Murthy, M
    Pedemonte, N
    MacVinish, L
    Galietta, L
    Cuthbert, A
    EUROPEAN JOURNAL OF PHARMACOLOGY, 2005, 516 (02) : 118 - 124
  • [24] DIRECT CARDIOVASCULAR EFFECTS OF THE CFTR ΔF508 MUTATION
    Roghair, R.
    McCray, P.
    Welsh, M.
    Santillan, D.
    Santillan, M.
    Stoltz, D. A.
    PEDIATRIC PULMONOLOGY, 2012, 47 : 288 - 289
  • [25] Benzbromarone Stabilizes ΔF508 CFTR at the Cell Surface
    Loo, Tip W.
    Bartlett, M. Claire
    Clarke, David M.
    BIOCHEMISTRY, 2011, 50 (21) : 4393 - 4395
  • [26] Processing correction and direct activation of ΔF508 CFTR by the flavonoid equol in vitro
    Rowe, S. M.
    Varga, K.
    Bebok, Z.
    Li, Y.
    Fan, L.
    Nowartowski, K.
    Prasin, J.
    Barnes, S.
    Clancy, J. P.
    Sorscher, E. J.
    PEDIATRIC PULMONOLOGY, 2007, : 299 - 299
  • [27] The unfolded protein response (UPR) pathway in Cryptococcus
    Cheon, Seon Ah
    Jung, Kwang-Woo
    Bahn, Yong-Sun
    Kang, Hyun Ah
    VIRULENCE, 2014, 5 (02) : 341 - 350
  • [28] MEASUREMENT OF THE UNFOLDED PROTEIN RESPONSE (UPR) IN MONOCYTES
    Carroll, Tomas P.
    Greene, Catherine M.
    McElvaney, Noel G.
    METHODS IN ENZYMOLOGY: UNFOLDED PROTEIN RESPONSE AND CELLULAR STRESS, VOL 489, PT A, 2011, 489 : 83 - 95
  • [29] THE ΔF508 MUTATION IN CFTR REDUCES THE PROINFLAMMATORY RESPONSE TO P. AERUGINOSA
    Hampton, T. H.
    Ballok, A. E.
    Rutkowski, M. R.
    Conejo-Garcia, J. R.
    O'Toole, G. A.
    Stanton, B. A.
    PEDIATRIC PULMONOLOGY, 2010, : 278 - 279
  • [30] Activation of the unfolded protein response (UPR) is required for adipogenic differentiation of preadipocytes
    Basseri, S
    Akhtar, M
    Ahmed, B
    Sood, S
    Colgan, S
    Austin, R
    Sharma, AM
    INTERNATIONAL JOURNAL OF OBESITY, 2005, 29 : S1 - S1