Acquired von Willebrand syndrome

被引:0
|
作者
Arabi, Abdessamad [1 ]
Taouli, Katia [2 ]
Chaffa, Ouardia [3 ]
Bekadja, Mohammad Amine [1 ]
机构
[1] Etablissement Hosp Univ 1Er Novembre 1954, Serv Hematol & Therapie Cellulaire, Ehu Oran, Algeria
[2] Ctr Hosp Univ, Serv Hemobiol, Tilimsen, Algeria
[3] Ctr Hosp Univ Mustapha, Serv Hemobiol, Algiers, Algeria
来源
SANG THROMBOSE VAISSEAUX | 2011年 / 23卷 / 06期
关键词
aquired von Willebrand syndrome; lymphoproliferative disorder and autoimmune disease; diagnosis; treatment;
D O I
10.1684/stv.2011.0614
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Acquired von Willebrand syndrome Acquired von Willebrand syndrome is rare disease, with clinical and biological features strikingly similar to the congenital form. 300 cases were reported in the literature. Most often, it occurs in old patients, ant it is frequently associated with autoimmune or lymphoproliferative disorders. Diagnosis is not difficult. According to literature, substitutive treatment is not efficient in all cases; etiologic treatment seems the better solution. Physiopathology is unknown. This is a case report of Acquired von Willebrand Syndrome diagnosed in a 62 old year man, without associated pathology.
引用
收藏
页码:303 / 306
页数:4
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