Duodenal atresia associated with the complete absence of small bowel

Duodenal atresia (DA) is one of the most common sites of neonatal intestinal obstruction and is frequently associated with various other anomalies. An isolated variant of DA has a better prognosis. Some associated intestinal abnormalities are not compatible with survival and definitive surgery could not be offered; however, these associated anomalies can be identified during laparotomy only. We present the case of a neonate with DA associated with the absence of the entire small bowel and also discuss its relevant embryology and pathology.