Manifestations of scleroderma pulmonary disease

被引:52
作者
Minai, OA [1 ]
Dweik, RA [1 ]
Arroliga, AC [1 ]
机构
[1] Cleveland Clin Fdn, Dept Pulm & Crit Care Med, Cleveland, OH 44195 USA
关键词
D O I
10.1016/S0272-5231(05)70112-X
中图分类号
R56 [呼吸系及胸部疾病];
学科分类号
摘要
Scleroderma is a multisystem disease of unknown cause characterized by synthesis and deposition of excessive extracellular matrix and vascular obliteration. Pulmonary involvement is a significant cause of morbidity and mortality. This article gives an overview of the pulmonary manifestations of scleroderma and discusses diagnostic and therapeutic options.
引用
收藏
页码:713 / +
页数:21
相关论文
共 169 条
[1]   CANCER IN SYSTEMIC-SCLEROSIS [J].
ABUSHAKRA, M ;
GUILLEMIN, F ;
LEE, P .
ARTHRITIS AND RHEUMATISM, 1993, 36 (04) :460-464
[2]  
ADHIKARI PK, 1962, AM REV RESPIR DIS, V86, P823
[3]   IMPROVED PULMONARY-FUNCTION IN SYSTEMIC-SCLEROSIS AFTER TREATMENT WITH CYCLOPHOSPHAMIDE [J].
AKESSON, A ;
SCHEJA, A ;
LUNDIN, A ;
WOLLHEIM, FA .
ARTHRITIS AND RHEUMATISM, 1994, 37 (05) :729-735
[4]   SHORT-TERM AND LONG-TERM HEMODYNAMIC-EFFECTS OF CAPTOPRIL IN PATIENTS WITH PULMONARY-HYPERTENSION AND SELECTED CONNECTIVE-TISSUE DISEASE [J].
ALPERT, MA ;
PRESSLY, TA ;
MUKERJI, V ;
LAMBERT, CR ;
MUKERJI, B .
CHEST, 1992, 102 (05) :1407-1412
[5]  
ALSABBAGH MR, 1989, J RHEUMATOL, V16, P1038
[6]   PREDICTORS OF SURVIVAL IN SYSTEMIC-SCLEROSIS (SCLERODERMA) [J].
ALTMAN, RD ;
MEDSGER, TA ;
BLOCH, DA ;
MICHEL, BA .
ARTHRITIS AND RHEUMATISM, 1991, 34 (04) :403-413
[7]   PULMONARY MANIFESTATIONS OF SCLERODERMA [J].
ARROLIGA, AC ;
PODELL, DN ;
MATTHAY, RA .
JOURNAL OF THORACIC IMAGING, 1992, 7 (02) :30-45
[8]   SERIAL PULMONARY-FUNCTION TESTS IN PROGRESSIVE SYSTEMIC-SCLEROSIS [J].
BAGG, LR ;
HUGHES, DTD .
THORAX, 1979, 34 (02) :224-228
[9]  
BARON M, 1982, BRIT HEART J, V48, P304
[10]   GA-67 LUNG SCANS IN PROGRESSIVE SYSTEMIC-SCLEROSIS [J].
BARON, M ;
FEIGLIN, D ;
HYLAND, R ;
UROWITZ, MB ;
SHIFF, B .
ARTHRITIS AND RHEUMATISM, 1983, 26 (08) :969-974