Severe malnutrition causing superior mesenteric artery syndrome in an adolescent with Triple A syndrome

被引：5

作者：

Foster, Christy ^{[2
]}

Choudhary, Abha ^{[1
]}

机构：

[1] UT Southwestern Med Ctr, Div Endocrinol, Dept Pediat, 5323 Harry Hines Blvd, Dallas, TX 75390 USA

[2] Arkansas Childrens Hosp, Dept Pediat, Little Rock, AR 72202 USA

来源：

JOURNAL OF PEDIATRIC ENDOCRINOLOGY & METABOLISM | 2016年 / 29卷 / 10期

关键词：

adrenal insufficiency; malnutrition; Triple A syndrome; A SYNDROME; ALLGROVE SYNDROME; GLUCOCORTICOID DEFICIENCY; AAAS GENE; ACHALASIA; MUTATIONS; FAMILY; ABNORMALITIES; DISEASE;

D O I：

10.1515/jpem-2015-0373

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

Triple A syndrome, formerly known as Allgrove syndrome (AS), is characterized by achalasia, alacrima and adrenal insufficiency. Here we report an adolescent male with adrenal insufficiency who developed severe malnutrition secondary to a delayed diagnosis of achalasia. The severe malnutrition in our patient led to superior mesenteric artery (SMA) obstruction syndrome. Severe malnutrition to the point of SMA syndrome has not been previously described in the literature in Triple A syndrome.

引用

页码：1221 / 1224

页数：4

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