Case Report: Life-Threatening Post-operative Hemorrhage in Klippel-Trenaunay Syndrome Associated With Hypofibrinogenemia

被引：1

作者：

Yang, Hongna ^{[1
]}

Du, Binfeng ^{[2
]}

Liu, Han ^{[2
]}

Yao, Yong ^{[2
]}

Li, Chen ^{[2
]}

机构：

[1] Shandong First Med Univ, Dept Crit Care Med, Shandong Prov Hosp, Jinan, Peoples R China

[2] Shandong Univ, Qilu Hosp, Dept Crit Care Med, Jinan, Peoples R China

来源：

FRONTIERS IN MEDICINE | 2021年 / 8卷

基金：

中国国家自然科学基金;

关键词：

conservative therapy; fibrinogen concentrate; hypofibrinogenemia; klipple-trenaunay syndrome; post-operative hemorrhage; prophylactic transfusion of fibrinogen; COAGULOPATHY; MANAGEMENT;

D O I：

10.3389/fmed.2021.669793

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

Klippel-Trenaunay Syndrome (KTS) is a rare congenital disorder, characterized by venous and lymphatic malformations of the skin, soft tissue, and bone, causing limb hypertrophy. Although, a ruptured hemorrhagic corpus luteum is a rare condition in women of reproductive age, it can result in lethal outcomes. Here, we have described a patient with KTS and hypofibrinogenemia who went through recurrent lethal postoperative bleeding due to a ruptured hemorrhagic corpus luteum. This case suggested that conservative therapy might be the first choice and effective therapy for the patients with KTS, who suffered from bleeding complications of surgical therapy.

引用

页数：4

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