An Unusual Coincidence of Subacute Sclerosing Panencephalitis and Duchenne Muscular Dystrophy

被引:0
作者
Kutlu, Ayse [1 ]
Korkmaz, Baris [2 ]
Yalcinkaya, Cengiz [2 ]
Demirbilek, Veysi [2 ]
Serdaroglu, Piraye [3 ]
机构
[1] Kocaeli Univ, Tip Fak, Kocaeli, Turkey
[2] Istanbul Univ, Cerrahpasa Tip Fak, Istanbul, Turkey
[3] Istanbul Univ, Istanbul Tip Fak, Istanbul, Turkey
来源
JOURNAL OF NEUROLOGICAL SCIENCES-TURKISH | 2010年 / 27卷 / 02期
关键词
SSPE; DMD; CPK; EEG; EPIDEMIOLOGY; ENGLAND;
D O I
暂无
中图分类号
Q189 [神经科学];
学科分类号
071006 ;
摘要
A 4 year old boy presented with myoclonic seizures, drop attacks and decrease in mental functions. Cranial MRI was normal. EEG revealed periodic slow wave complexes and subsequent CSF analysis showed positive antimeasles IgG. CPK was also markedly abnormal (10.000 u/L). Muscle biopsy and genetic analysis displayed the presence of DMD. The case was interpreted as an unusual coincidence of SSPE and DMD
引用
收藏
页码:250 / 253
页数:4
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