Congenital bile duct dilatation (CBD) that developed in a parent and son is presented. Familial occurrence of CBD is rare, with only a few male cases having been reported. Since the initial report of CBD occurring in siblings in 1981, a total of 20 cases (10 pairs) have been published as of 2007. Clinical and genetic features of CBD are discussed. (C) 2008 WJG. All rights reserved.
机构:
Tokyo Med Univ, Dept Gastrointestinal & Pediat Surg, Shinjuku Ku, 6-7-1 Nishi Shinjuku, Tokyo 1600023, JapanTokyo Med Univ, Dept Gastrointestinal & Pediat Surg, Shinjuku Ku, 6-7-1 Nishi Shinjuku, Tokyo 1600023, Japan
Kiya, Yoshitaka
Nagakawa, Yuichi
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Tokyo Med Univ, Dept Gastrointestinal & Pediat Surg, Shinjuku Ku, 6-7-1 Nishi Shinjuku, Tokyo 1600023, JapanTokyo Med Univ, Dept Gastrointestinal & Pediat Surg, Shinjuku Ku, 6-7-1 Nishi Shinjuku, Tokyo 1600023, Japan
Nagakawa, Yuichi
Takishita, Chie
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Tokyo Med Univ, Dept Gastrointestinal & Pediat Surg, Shinjuku Ku, 6-7-1 Nishi Shinjuku, Tokyo 1600023, JapanTokyo Med Univ, Dept Gastrointestinal & Pediat Surg, Shinjuku Ku, 6-7-1 Nishi Shinjuku, Tokyo 1600023, Japan
Takishita, Chie
Osakabe, Hiroaki
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Tokyo Med Univ, Dept Gastrointestinal & Pediat Surg, Shinjuku Ku, 6-7-1 Nishi Shinjuku, Tokyo 1600023, JapanTokyo Med Univ, Dept Gastrointestinal & Pediat Surg, Shinjuku Ku, 6-7-1 Nishi Shinjuku, Tokyo 1600023, Japan
Osakabe, Hiroaki
Nishino, Hitoe
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Tokyo Med Univ, Dept Gastrointestinal & Pediat Surg, Shinjuku Ku, 6-7-1 Nishi Shinjuku, Tokyo 1600023, JapanTokyo Med Univ, Dept Gastrointestinal & Pediat Surg, Shinjuku Ku, 6-7-1 Nishi Shinjuku, Tokyo 1600023, Japan
Nishino, Hitoe
Akashi, Masanori
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Kurume Univ, Dept Surg, Sch Med, 67 Asahicho, Kurume, Fukuoka 8300011, JapanTokyo Med Univ, Dept Gastrointestinal & Pediat Surg, Shinjuku Ku, 6-7-1 Nishi Shinjuku, Tokyo 1600023, Japan
Akashi, Masanori
Yamaguchi, Hiroshi
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Saitama Med Univ, Dept Pathol, 38 Morohongo, Moroyama, Saitama 3500495, JapanTokyo Med Univ, Dept Gastrointestinal & Pediat Surg, Shinjuku Ku, 6-7-1 Nishi Shinjuku, Tokyo 1600023, Japan
Yamaguchi, Hiroshi
Nagao, Toshitaka
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Tokyo Med Univ, Dept Anat Pathol, Shinjuku Ku, 6-7-1 Nishi Shinjuku, Tokyo 1600023, JapanTokyo Med Univ, Dept Gastrointestinal & Pediat Surg, Shinjuku Ku, 6-7-1 Nishi Shinjuku, Tokyo 1600023, Japan
Nagao, Toshitaka
Oono, Ryo
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机构:
Nitobe Mem Nakano Gen Hosp, Dept Digest Surg, Nakano Ku, 4-59-16 Chuo, Tokyo 1648607, JapanTokyo Med Univ, Dept Gastrointestinal & Pediat Surg, Shinjuku Ku, 6-7-1 Nishi Shinjuku, Tokyo 1600023, Japan
Oono, Ryo
Katsumata, Kenji
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Tokyo Med Univ, Dept Gastrointestinal & Pediat Surg, Shinjuku Ku, 6-7-1 Nishi Shinjuku, Tokyo 1600023, JapanTokyo Med Univ, Dept Gastrointestinal & Pediat Surg, Shinjuku Ku, 6-7-1 Nishi Shinjuku, Tokyo 1600023, Japan
Katsumata, Kenji
Tsuchida, Akihiko
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Tokyo Med Univ, Dept Gastrointestinal & Pediat Surg, Shinjuku Ku, 6-7-1 Nishi Shinjuku, Tokyo 1600023, JapanTokyo Med Univ, Dept Gastrointestinal & Pediat Surg, Shinjuku Ku, 6-7-1 Nishi Shinjuku, Tokyo 1600023, Japan
机构:
West China Hosp, Shangjin Nanfu Branch, Operat Anesthesia Ctr, Chengdu 610041, Sichuan, Peoples R ChinaWest China Hosp, Shangjin Nanfu Branch, Operat Anesthesia Ctr, Chengdu 610041, Sichuan, Peoples R China
Wei, Mingfeng
Wu, Haojun
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机构:
Sichuan Univ, West China Hosp, Dept Gen Surg, Div Biliary Surg, Chengdu 610041, Sichuan, Peoples R ChinaWest China Hosp, Shangjin Nanfu Branch, Operat Anesthesia Ctr, Chengdu 610041, Sichuan, Peoples R China
Wu, Haojun
Chen, Liping
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Sichuan Univ, West China Hosp, Dept Gen Surg, Div Biliary Surg, Chengdu 610041, Sichuan, Peoples R ChinaWest China Hosp, Shangjin Nanfu Branch, Operat Anesthesia Ctr, Chengdu 610041, Sichuan, Peoples R China
Chen, Liping
Liu, Ziming
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Sichuan Univ, West China Hosp, Dept Gen Surg, Div Biliary Surg, Chengdu 610041, Sichuan, Peoples R ChinaWest China Hosp, Shangjin Nanfu Branch, Operat Anesthesia Ctr, Chengdu 610041, Sichuan, Peoples R China
机构:
Department of Pediatric Surgery, Kansai Medical University, 2-3-1 Shinmachi, Osaka, HirakataDepartment of Pediatric Surgery, Kansai Medical University, 2-3-1 Shinmachi, Osaka, Hirakata
Takeshi Shirai
Yoshinori Hamada
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Department of Pediatric Surgery, Kansai Medical University, 2-3-1 Shinmachi, Osaka, HirakataDepartment of Pediatric Surgery, Kansai Medical University, 2-3-1 Shinmachi, Osaka, Hirakata
Yoshinori Hamada
Hiroshi Hamada
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Department of Pediatric Surgery, Kansai Medical University, 2-3-1 Shinmachi, Osaka, HirakataDepartment of Pediatric Surgery, Kansai Medical University, 2-3-1 Shinmachi, Osaka, Hirakata
Hiroshi Hamada
Takashi Doi
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机构:
Department of Pediatric Surgery, Kansai Medical University, 2-3-1 Shinmachi, Osaka, HirakataDepartment of Pediatric Surgery, Kansai Medical University, 2-3-1 Shinmachi, Osaka, Hirakata