Syndromic presentatton of a pleuropulmonary Blastoma associated with congenital cystic adenomatoid malformation. A case report

被引：17

作者：

Nur, Samina

Badr, Riem

Sandoval, Claudio

Brudniki, Adele

Yeh, Albert

机构：

[1] New York Med Coll, Westchester Cty Med Ctr, Dept Pathol, Valhalla, NY 10595 USA

[2] New York Med Coll, Westchester Cty Med Ctr, Dept Pediat Oncol, Valhalla, NY 10595 USA

[3] New York Med Coll, Westchester Cty Med Ctr, Dept Radiol, Valhalla, NY 10595 USA

来源：

JOURNAL OF PEDIATRIC SURGERY | 2007年 / 42卷 / 10期

关键词：

pleuropulmonary blastoma; cystic adenomatoid malformation; brain metastasis; hamartomatous polyps; recurrent intussusception;

D O I：

10.1016/j.jpedsurg.2007.06.022

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

Pleuropulmonary blastoma (PPB) is a rare malignant mesenchymal pediatric tumor with a well-recognized association with congenital cystic adenomatoid malformation (CCAM). Recently, it has been described in a patient with CCAM, multiple jejunal polyps, and cystic nephroma. We describe a similar case of a unique presentation of PPB, arising in association with CCAM and with a history of intussception caused by multiple small bowel polyps. (C) 2007 Elsevier Inc. All rights reserved.

引用

页码：1772 / 1775

页数：4

共 16 条

[1] Familial association of pleuropulmonary blastoma with cystic nephroma and other renal tumors: A report from the international pleuropulmonary blastoma registry [J].