Syndromic presentatton of a pleuropulmonary Blastoma associated with congenital cystic adenomatoid malformation. A case report

被引：17
作者：
Nur, Samina
Badr, Riem
Sandoval, Claudio
Brudniki, Adele
Yeh, Albert
机构：
[1] New York Med Coll, Westchester Cty Med Ctr, Dept Pathol, Valhalla, NY 10595 USA
[2] New York Med Coll, Westchester Cty Med Ctr, Dept Pediat Oncol, Valhalla, NY 10595 USA
[3] New York Med Coll, Westchester Cty Med Ctr, Dept Radiol, Valhalla, NY 10595 USA
来源：
JOURNAL OF PEDIATRIC SURGERY | 2007年 / 42卷 / 10期
关键词：
pleuropulmonary blastoma; cystic adenomatoid malformation; brain metastasis; hamartomatous polyps; recurrent intussusception;
D O I：
10.1016/j.jpedsurg.2007.06.022
中图分类号：
R72 [儿科学];
学科分类号：
100202 ;
摘要：
Pleuropulmonary blastoma (PPB) is a rare malignant mesenchymal pediatric tumor with a well-recognized association with congenital cystic adenomatoid malformation (CCAM). Recently, it has been described in a patient with CCAM, multiple jejunal polyps, and cystic nephroma. We describe a similar case of a unique presentation of PPB, arising in association with CCAM and with a history of intussception caused by multiple small bowel polyps. (C) 2007 Elsevier Inc. All rights reserved.
引用
收藏
页码：1772 / 1775
页数：4
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