Epidermolysis Bullosa is a genetic disorder that affects mainly the skin, however, all others systems are influenced. The nutritional care of children and adolescents with Epidermolysis Bullosa is a key treatment strategy, since the energy needs are increased due to the disease's metabolism, burdening the immune system and cicatrization process, symptoms caused by the disease hinder the intake and adequate absorption of nutrients, which may result in inadequate growth and development. Because this is a rare disease, there are few professionals who know the characteristics of both the clinical evolution and nutritional and dietary treatments. This literature review discusses the latest knowledge on energy and specific nutrient requirements to the dietary treatment and monitoring of children and adolescents with Epidermolysis Bullosa.
机构:Krisline Birge is a clinic nutritionist at the Stanford University Medical Center, Department of Nutrition and Foodservice HI209, Stanford, CA 94305
机构:
Univ Paris 05, Hop Necker Enfants Malad, AP HP,French Reference Ctr Rare Digest Dis, Dept Paediat Gastroenterol & Nutr,Nutr Support Te, F-75015 Paris, FranceUniv Paris 05, French Reference Ctr Genet Skin Disorders MAGEC, Hop Necker Enfants Malad, AP HP,Dept Dermatol, F-75015 Paris, France
Colomb, V.
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Bourdon-Lannoy, E.
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Univ Paris 05, French Reference Ctr Genet Skin Disorders MAGEC, Hop Necker Enfants Malad, AP HP,Dept Dermatol, F-75015 Paris, FranceUniv Paris 05, French Reference Ctr Genet Skin Disorders MAGEC, Hop Necker Enfants Malad, AP HP,Dept Dermatol, F-75015 Paris, France
Bourdon-Lannoy, E.
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Lambe, C.
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Sauvat, F.
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Univ Paris 05, Hop Necker Enfants Malad, AP HP, Dept Paediat Surg, F-75015 Paris, FranceUniv Paris 05, French Reference Ctr Genet Skin Disorders MAGEC, Hop Necker Enfants Malad, AP HP,Dept Dermatol, F-75015 Paris, France
Sauvat, F.
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Rabia, S. Hadj
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h-index: 0
机构:
Univ Paris 05, French Reference Ctr Genet Skin Disorders MAGEC, Hop Necker Enfants Malad, AP HP,Dept Dermatol, F-75015 Paris, FranceUniv Paris 05, French Reference Ctr Genet Skin Disorders MAGEC, Hop Necker Enfants Malad, AP HP,Dept Dermatol, F-75015 Paris, France
Rabia, S. Hadj
;
Teillac, D.
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h-index: 0
机构:
Univ Paris 05, French Reference Ctr Genet Skin Disorders MAGEC, Hop Necker Enfants Malad, AP HP,Dept Dermatol, F-75015 Paris, FranceUniv Paris 05, French Reference Ctr Genet Skin Disorders MAGEC, Hop Necker Enfants Malad, AP HP,Dept Dermatol, F-75015 Paris, France
Teillac, D.
;
De Prost, Y.
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h-index: 0
机构:
Univ Paris 05, French Reference Ctr Genet Skin Disorders MAGEC, Hop Necker Enfants Malad, AP HP,Dept Dermatol, F-75015 Paris, FranceUniv Paris 05, French Reference Ctr Genet Skin Disorders MAGEC, Hop Necker Enfants Malad, AP HP,Dept Dermatol, F-75015 Paris, France
De Prost, Y.
;
Bodemer, C.
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h-index: 0
机构:
Univ Paris 05, French Reference Ctr Genet Skin Disorders MAGEC, Hop Necker Enfants Malad, AP HP,Dept Dermatol, F-75015 Paris, FranceUniv Paris 05, French Reference Ctr Genet Skin Disorders MAGEC, Hop Necker Enfants Malad, AP HP,Dept Dermatol, F-75015 Paris, France
机构:
Great Ormond St Hosp Sick Children, Dept Paediat Gastroenterol, London WC1N 3JH, EnglandGreat Ormond St Hosp Sick Children, Dept Paediat Gastroenterol, London WC1N 3JH, England
Freeman, E. B.
;
Koglmeier, J.
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h-index: 0
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Great Ormond St Hosp Sick Children, Dept Paediat Gastroenterol, London WC1N 3JH, EnglandGreat Ormond St Hosp Sick Children, Dept Paediat Gastroenterol, London WC1N 3JH, England
Koglmeier, J.
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Martinez, A. E.
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h-index: 0
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Great Ormond St Hosp Sick Children, Dept Paediat Dermatol, London WC1N 3JH, EnglandGreat Ormond St Hosp Sick Children, Dept Paediat Gastroenterol, London WC1N 3JH, England
Martinez, A. E.
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Mellerio, J. E.
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h-index: 0
机构:
Great Ormond St Hosp Sick Children, Dept Paediat Dermatol, London WC1N 3JH, EnglandGreat Ormond St Hosp Sick Children, Dept Paediat Gastroenterol, London WC1N 3JH, England
Mellerio, J. E.
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Haynes, L.
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Great Ormond St Hosp Sick Children, Dept Dietet, London WC1N 3JH, EnglandGreat Ormond St Hosp Sick Children, Dept Paediat Gastroenterol, London WC1N 3JH, England
Haynes, L.
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Sebire, N. J.
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Great Ormond St Hosp Sick Children, Dept Histopathol, London WC1N 3JH, EnglandGreat Ormond St Hosp Sick Children, Dept Paediat Gastroenterol, London WC1N 3JH, England
Sebire, N. J.
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Lindley, K. J.
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h-index: 0
机构:
Great Ormond St Hosp Sick Children, Dept Paediat Gastroenterol, London WC1N 3JH, EnglandGreat Ormond St Hosp Sick Children, Dept Paediat Gastroenterol, London WC1N 3JH, England
Lindley, K. J.
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Shah, N.
论文数: 0引用数: 0
h-index: 0
机构:
Great Ormond St Hosp Sick Children, Dept Paediat Gastroenterol, London WC1N 3JH, EnglandGreat Ormond St Hosp Sick Children, Dept Paediat Gastroenterol, London WC1N 3JH, England
机构:Krisline Birge is a clinic nutritionist at the Stanford University Medical Center, Department of Nutrition and Foodservice HI209, Stanford, CA 94305
机构:
Univ Paris 05, Hop Necker Enfants Malad, AP HP,French Reference Ctr Rare Digest Dis, Dept Paediat Gastroenterol & Nutr,Nutr Support Te, F-75015 Paris, FranceUniv Paris 05, French Reference Ctr Genet Skin Disorders MAGEC, Hop Necker Enfants Malad, AP HP,Dept Dermatol, F-75015 Paris, France
Colomb, V.
;
Bourdon-Lannoy, E.
论文数: 0引用数: 0
h-index: 0
机构:
Univ Paris 05, French Reference Ctr Genet Skin Disorders MAGEC, Hop Necker Enfants Malad, AP HP,Dept Dermatol, F-75015 Paris, FranceUniv Paris 05, French Reference Ctr Genet Skin Disorders MAGEC, Hop Necker Enfants Malad, AP HP,Dept Dermatol, F-75015 Paris, France
Bourdon-Lannoy, E.
;
论文数: 引用数:
h-index:
机构:
Lambe, C.
;
Sauvat, F.
论文数: 0引用数: 0
h-index: 0
机构:
Univ Paris 05, Hop Necker Enfants Malad, AP HP, Dept Paediat Surg, F-75015 Paris, FranceUniv Paris 05, French Reference Ctr Genet Skin Disorders MAGEC, Hop Necker Enfants Malad, AP HP,Dept Dermatol, F-75015 Paris, France
Sauvat, F.
;
Rabia, S. Hadj
论文数: 0引用数: 0
h-index: 0
机构:
Univ Paris 05, French Reference Ctr Genet Skin Disorders MAGEC, Hop Necker Enfants Malad, AP HP,Dept Dermatol, F-75015 Paris, FranceUniv Paris 05, French Reference Ctr Genet Skin Disorders MAGEC, Hop Necker Enfants Malad, AP HP,Dept Dermatol, F-75015 Paris, France
Rabia, S. Hadj
;
Teillac, D.
论文数: 0引用数: 0
h-index: 0
机构:
Univ Paris 05, French Reference Ctr Genet Skin Disorders MAGEC, Hop Necker Enfants Malad, AP HP,Dept Dermatol, F-75015 Paris, FranceUniv Paris 05, French Reference Ctr Genet Skin Disorders MAGEC, Hop Necker Enfants Malad, AP HP,Dept Dermatol, F-75015 Paris, France
Teillac, D.
;
De Prost, Y.
论文数: 0引用数: 0
h-index: 0
机构:
Univ Paris 05, French Reference Ctr Genet Skin Disorders MAGEC, Hop Necker Enfants Malad, AP HP,Dept Dermatol, F-75015 Paris, FranceUniv Paris 05, French Reference Ctr Genet Skin Disorders MAGEC, Hop Necker Enfants Malad, AP HP,Dept Dermatol, F-75015 Paris, France
De Prost, Y.
;
Bodemer, C.
论文数: 0引用数: 0
h-index: 0
机构:
Univ Paris 05, French Reference Ctr Genet Skin Disorders MAGEC, Hop Necker Enfants Malad, AP HP,Dept Dermatol, F-75015 Paris, FranceUniv Paris 05, French Reference Ctr Genet Skin Disorders MAGEC, Hop Necker Enfants Malad, AP HP,Dept Dermatol, F-75015 Paris, France
机构:
Great Ormond St Hosp Sick Children, Dept Paediat Gastroenterol, London WC1N 3JH, EnglandGreat Ormond St Hosp Sick Children, Dept Paediat Gastroenterol, London WC1N 3JH, England
Freeman, E. B.
;
Koglmeier, J.
论文数: 0引用数: 0
h-index: 0
机构:
Great Ormond St Hosp Sick Children, Dept Paediat Gastroenterol, London WC1N 3JH, EnglandGreat Ormond St Hosp Sick Children, Dept Paediat Gastroenterol, London WC1N 3JH, England
Koglmeier, J.
;
Martinez, A. E.
论文数: 0引用数: 0
h-index: 0
机构:
Great Ormond St Hosp Sick Children, Dept Paediat Dermatol, London WC1N 3JH, EnglandGreat Ormond St Hosp Sick Children, Dept Paediat Gastroenterol, London WC1N 3JH, England
Martinez, A. E.
;
Mellerio, J. E.
论文数: 0引用数: 0
h-index: 0
机构:
Great Ormond St Hosp Sick Children, Dept Paediat Dermatol, London WC1N 3JH, EnglandGreat Ormond St Hosp Sick Children, Dept Paediat Gastroenterol, London WC1N 3JH, England
Mellerio, J. E.
;
Haynes, L.
论文数: 0引用数: 0
h-index: 0
机构:
Great Ormond St Hosp Sick Children, Dept Dietet, London WC1N 3JH, EnglandGreat Ormond St Hosp Sick Children, Dept Paediat Gastroenterol, London WC1N 3JH, England
Haynes, L.
;
Sebire, N. J.
论文数: 0引用数: 0
h-index: 0
机构:
Great Ormond St Hosp Sick Children, Dept Histopathol, London WC1N 3JH, EnglandGreat Ormond St Hosp Sick Children, Dept Paediat Gastroenterol, London WC1N 3JH, England
Sebire, N. J.
;
Lindley, K. J.
论文数: 0引用数: 0
h-index: 0
机构:
Great Ormond St Hosp Sick Children, Dept Paediat Gastroenterol, London WC1N 3JH, EnglandGreat Ormond St Hosp Sick Children, Dept Paediat Gastroenterol, London WC1N 3JH, England
Lindley, K. J.
;
Shah, N.
论文数: 0引用数: 0
h-index: 0
机构:
Great Ormond St Hosp Sick Children, Dept Paediat Gastroenterol, London WC1N 3JH, EnglandGreat Ormond St Hosp Sick Children, Dept Paediat Gastroenterol, London WC1N 3JH, England