Neurofibroma of the bladder wall in von Recklinghausen's disease

被引:4
作者
Aygun, C
Tekin, MI
Tarhan, C
Ozdemir, H
Peskircioglu, L
Ozkardes, H
机构
[1] Baskent Univ, Sch Med, Dept Urol, TR-06490 Ankara, Turkey
[2] Baskent Univ, Sch Med, Dept Radiol, TR-06490 Ankara, Turkey
[3] Baskent Univ, Sch Med, Dept Pathol, TR-06490 Ankara, Turkey
关键词
neurofibroma; neurofibromatosis; urinary bladder;
D O I
10.1046/j.1442-2042.2001.00294.x
中图分类号
R5 [内科学]; R69 [泌尿科学(泌尿生殖系疾病)];
学科分类号
1002 ; 100201 ;
摘要
Neurofibromatosis, or von Recklinghausen's disease, is an autosomal dominant disease with multiple neurofibroma and cafe-au-lait spots. However, neurofibroma in the bladder wall is a rare condition in von Recklinghausen's disease. A 31-year-old man with neurogenic voiding dysfunction due to sacral meningocele and acute urinary retention with neurofibroma of the bladder wall is presented with detailed radiologic evaluation. Patients with von Recklinghausen's disease should be carefully evaluated if urological symptoms exist.
引用
收藏
页码:249 / 253
页数:5
相关论文
共 18 条
[1]   GENE FOR VON RECKLINGHAUSEN NEUROFIBROMATOSIS IS IN THE PERICENTROMERIC REGION OF CHROMOSOME-17 [J].
BARKER, D ;
WRIGHT, E ;
NGUYEN, K ;
CANNON, L ;
FAIN, P ;
GOLDGAR, D ;
BISHOP, DT ;
CAREY, J ;
BATY, B ;
KIVLIN, J ;
WILLARD, H ;
WAYE, JS ;
GREIG, G ;
LEINWAND, L ;
NAKAMURA, Y ;
OCONNELL, P ;
LEPPERT, M ;
LALOUEL, JM ;
WHITE, R ;
SKOLNICK, M .
SCIENCE, 1987, 236 (4805) :1100-1102
[2]   UROLOGIC MANIFESTATIONS OF VONRECKLINGHAUSEN NEUROFIBROMATOSIS [J].
BLUM, MD ;
BAHNSON, RR ;
CARTER, MF .
UROLOGY, 1985, 26 (03) :209-217
[3]  
DAHM P, 1995, EUR UROL, V27, P261
[4]   PELVIC NEUROFIBROMATOSIS - LOCALIZED VON RECKLINGHAUSENS DISEASE OF BLADDER [J].
DENIZ, E ;
SHIMKUS, GJ ;
WELLER, CG .
JOURNAL OF UROLOGY, 1966, 96 (06) :906-&
[5]  
GERHARDT C, 1878, DTSCH ARCH KLIN MED, V21, P268
[6]  
GOLDBERG NS, 1996, CUTANEOUS MED SURG I, P1729
[8]   NEUROFIBROMATOSIS - BLADDER INVOLVEMENT WITH MALIGNANT DEGENERATION [J].
HULSE, CA .
JOURNAL OF UROLOGY, 1990, 144 (03) :742-743
[9]   INFLAMMATORY PSEUDOTUMOR OF THE URINARY-BLADDER - A CLINICOPATHOLOGICAL, IMMUNOHISTOCHEMICAL, ULTRASTRUCTURAL, AND FLOW CYTOMETRIC STUDY OF 13 CASES [J].
JONES, EC ;
CLEMENT, PB ;
YOUNG, RH .
AMERICAN JOURNAL OF SURGICAL PATHOLOGY, 1993, 17 (03) :264-274
[10]  
LEE JKT, 1998, COMPUTED BODY TOMOGR, V20, P1209