Real-world use of inhaled treprostinil for lung disease-pulmonary hypertension: A protocol for patient evaluation and prescribing

被引：8

作者：

Johnson, Shelsey W. ^{[1
,2
]}

Finlay, Lauren ^{[3
]}

Mathai, Stephen C. ^{[4
,5
]}

Goldstein, Ronald H. ^{[1
,2
]}

Maron, Bradley A. ^{[1
,6
,7
]}

机构：

[1] VA Boston Healthcare Syst, Dept Pulm Allergy Sleep & Crit Care Med, 77 Ave Louis Pasteur,NRB 0630-N, Boston, MA 02115 USA

[2] Boston Univ, Sch Med, Ctr Pulm, Div Pulm Allergy Sleep & Crit Care, Boston, MA 02215 USA

[3] VA Boston Healthcare Syst, Dept Pharm, Boston, MA USA

[4] Johns Hopkins Univ, Dept Pulm & Crit Care Med, Baltimore, MD USA

[5] Johns Hopkins Sch Med, Baltimore, MD USA

[6] Brigham & Womens Hosp, Div Cardiovasc Med, 75 Francis St, Boston, MA 02115 USA

[7] Harvard Med Sch, Boston, MA 02115 USA

来源：

PULMONARY CIRCULATION | 2022年 / 12卷 / 03期

关键词：

Group 3 pulmonary hypertension; inhaled treprostinil; interstitial lung disease; pulmonary hypertension; ARTERIAL-HYPERTENSION; THERAPY; CAPACITY; OUTCOMES;

D O I：

10.1002/pul2.12126

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

Inhaled treprostinil was approved recently for interstitial lung disease-pulmonary hypertension; however, efficacy in "real-world" populations is not known. We designed a protocol and report our experience evaluating 10 patients referred for therapy. Misdiagnosis at presentation was common; ultimately, three patients (30%) were prescribed drug. This protocol offers an opportunity to standardize longitudinal assessment of inhaled treprostinil in clinical practice.

引用

页数：7

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