Living donor liver transplantation for hepatoblastoma with Beckwith-Wiedemann syndrome

被引：1

作者：

Sasaki, Kazunari ^{[1
]}

Kasahara, Mureo ^{[1
]}

Fukuda, Akinari ^{[1
]}

Shigeta, Takanobu ^{[1
]}

Tanaka, Hideaki ^{[2
]}

Nakagawa, Satoshi ^{[3
]}

Mitsui, Kazumasa ^{[4
]}

Harada, Ryoko ^{[4
]}

Nakagawa, Atsuko ^{[5
]}

机构：

[1] Natl Ctr Child Hlth & Dev, Dept Transplantat Surg, Tokyo, Japan

[2] Natl Ctr Child Hlth & Dev, Dept Pediat Surg, Tokyo, Japan

[3] Natl Ctr Child Hlth & Dev, Dept Intens Care, Tokyo, Japan

[4] Toho Univ, Omori Med Ctr, Dept Pediat, Tokyo, Japan

[5] Natl Ctr Child Hlth & Dev, Dept Pathol, Tokyo, Japan

来源：

PEDIATRIC TRANSPLANTATION | 2010年 / 14卷 / 07期

关键词：

Beckwith-Wiedemann; transplantation; hepatoblastoma; INTERNATIONAL-SOCIETY; MODERN-ERA; TUMOR; GUIDELINES; CHILDREN; RISK;

D O I：

10.1111/j.1399-3046.2009.01198.x

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

BWS is one of the most well-known somatic overgrowth syndromes, which is characterized by macroglossia, organomegaly, abdominal wall defects, and predisposition to embryonal tumors, such as Wilms' tumor, hepatoblastoma, and adrenocortical carcinoma. We report a case of BWS in a girl with unresectable hepatoblastoma, who received a planned LVDT following neo-adjuvant chemotherapy. This is the first case report of liver transplantation for patients with BWS. Tumor surveillance after transplantation would be necessary to detect possible recurrence of the original disease and development of other malignancies.

引用

页码：E89 / E92

页数：4

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