Cystic fibrosis papers of the year 2017

被引：2
|
作者：
Doull, Iolo [1 ,2 ]
机构：
[1] Childrens Hosp Wales, Dept Paediat Resp Med, Cardiff CF14 4XN, S Glam, Wales
[2] Childrens Hosp Wales, Paediat Cyst Fibrosis Ctr, Cardiff CF14 4XN, S Glam, Wales
来源：
PAEDIATRIC RESPIRATORY REVIEWS | 2018年 / 27卷
关键词：
Cystic fibrosis; Ivacaftor; Lumacaftor; Tezacaftor; Doxycycline; MRSA; RESISTANT STAPHYLOCOCCUS-AUREUS; PHE508DEL CFTR MUTATION; AGED; 6-11; YEARS; TEZACAFTOR-IVACAFTOR; LUNG-FUNCTION; LUMACAFTOR/IVACAFTOR; EFFICACY; F508DEL-CFTR; COMBINATION; PHASE-3;
D O I：
10.1016/j.prrv.2018.03.001
中图分类号：
R72 [儿科学];
学科分类号：
100202 ;
摘要：
The number of published articles on Cystic Fibrosis (CF) continues to increase year on year. The evidence base for small molecule therapies in CF has continued to expand, with evidence for lumacaftor/ivacaftor in younger patients and longer-term evidence in adults, and pivotal studies on tezacaftor/ivacaftor. There were reports on emerging CFTR mutation agnostic therapies, and new evidence for long standing therapies. (C) 2018 Elsevier Ltd. All rights reserved.
引用
收藏
页码：2 / 5
页数：4
相关论文
共 50 条
  • [41] Year in Review 2020: Multisystemic impact of cystic fibrosis
    Sharma, Preeti B.
    Sathe, Meghana
    Savant, Adrienne P.
    PEDIATRIC PULMONOLOGY, 2021, 56 (10) : 3110 - 3119
  • [42] Cystic fibrosis year in review 2018, part 1
    Savant, Adrienne P.
    McColley, Susanna A.
    PEDIATRIC PULMONOLOGY, 2019, 54 (08) : 1117 - 1128
  • [43] The Irish cystic fibrosis database - a year 2000 update
    McQuaid, SA
    Joyce, C
    Ward, AJ
    Ryan, F
    Clabby, C
    McDevitt, TM
    Cockburn, DJ
    Barton, DE
    JOURNAL OF MEDICAL GENETICS, 2000, 37 : S76 - S76
  • [44] CYSTIC-FIBROSIS IN A 70 YEAR OLD WOMAN
    VANBIEZEN, P
    OVERBEEK, SE
    HILVERING, C
    THORAX, 1992, 47 (03) : 202 - 203
  • [45] Fifty-year perspective of "cystic fibrosis of the pancreas"
    Spock, A
    PEDIATRIC RADIOLOGY, 2005, 35 (08) : 735 - 738
  • [46] Fifty-year perspective of “cystic fibrosis of the pancreas”
    Alexander Spock
    Pediatric Radiology, 2005, 35 : 735 - 738
  • [47] Cystic fibrosis in the year 2020: A disease with a new face
    De Boeck, Kris
    ACTA PAEDIATRICA, 2020, 109 (05) : 893 - 899
  • [48] ntroduction to 'Cystic Fibrosis Foundation Consensus Guidelines for Diagnosis of Cystic Fibrosis' (vol 181, pg S1, 2017)
    Farrell, P. M.
    JOURNAL OF PEDIATRICS, 2017, 184 : 243 - 243
  • [49] Non-invasive Ventilation in Cystic Fibrosis: A 23-year Analysis of the Australian Cystic Fibrosis Data Registry
    Gardiner, A.
    McGuiness, O.
    Menadue, C.
    Aquino-Salomon, T.
    Bortoft, K.
    Hammond, K.
    Visser, S.
    Jo, H.
    Yozghatlian, V.
    Yee, B. J.
    Wong, K. K.
    Piper, A. J.
    Sivam, S.
    AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE, 2024, 209
  • [50] Gastrointestinal surgery in cystic fibrosis: A 20-year review
    Farrelly, Paul J.
    Charlesworth, Caroline
    Lee, Sophie
    Southern, Kevin W.
    Baillie, Colin T.
    JOURNAL OF PEDIATRIC SURGERY, 2014, 49 (02) : 280 - 283
12345