Pulmonary atresia with intact ventricular septum and coronary cameral fistulae: an unusual finding of a subsystemic right ventricle

被引：1
|
作者：
Mohan, Shaun [1 ]
Weinberg, Paul M. [1 ]
Glatz, Andrew C. [1 ,2 ]
机构：
[1] Univ Penn, Perelman Sch Med, Childrens Hosp Philadelphia, Dept Pediat,Div Cardiol, 6th Floor,Main Bldg,34th St & Civ Ctr Blvd, Philadelphia, PA 19104 USA
[2] Univ Penn, Perelman Sch Med, Ctr Clin Epidemiol & Biostat, Philadelphia, PA 19104 USA
来源：
CARDIOLOGY IN THE YOUNG | 2016年 / 26卷 / 05期
关键词：
Pulmonary atresia; intact septum; coronary cameral fistulae; CIRCULATION; MANAGEMENT;
D O I：
10.1017/S1047951115002711
中图分类号：
R5 [内科学];
学科分类号：
1002 ; 100201 ;
摘要：
We report the case of a neonate with pulmonary atresia with intact ventricular septum and coronary cameral fistulae despite having a subsystemic right ventricle. We review the literature on coronary cameral fistulae in this disease and right ventricle-dependent coronary circulation. We discuss the potential consequences of this physiology, including risk of adverse cardiovascular events that may impact risk stratification and surgical palliation.
引用
收藏
页码：979 / 982
页数：4
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