A to Z of Desmoid Tumors

被引:96
|
作者
Shinagare, Atul B. [1 ,2 ]
Ramaiya, Nikhil H. [1 ,2 ]
Jagannathan, Jyothi P. [1 ,2 ]
Krajewski, Katherine M. [1 ,2 ]
Giardino, Angela A. [1 ,2 ]
Butrynski, James E. [3 ]
Raut, Chandrajit P. [4 ]
机构
[1] Brigham & Womens Hosp, Dana Farber Canc Inst, Dept Imaging, Boston, MA 02215 USA
[2] Brigham & Womens Hosp, Dept Radiol, Boston, MA 02215 USA
[3] Harvard Univ, Sch Med, Dana Farber Canc Inst, Dept Med Oncol, Boston, MA 02115 USA
[4] Harvard Univ, Brigham & Womens Hosp, Sch Med, Dept Surg, Boston, MA 02115 USA
关键词
complications; deep fibromatosis; desmoid tumors; extraabdominal desmoids; treatment-related changes; FIBROMATOSIS; THERAPY; FEATURES;
D O I
10.2214/AJR.11.6657
中图分类号
R8 [特种医学]; R445 [影像诊断学];
学科分类号
1002 ; 100207 ; 1009 ;
摘要
OBJECTIVE. The purpose of this article is to illustrate the common locations of desmoid tumors (deep fibromatosis), complications of intra-and extraabdominal desmoids, and treatment-related changes in their imaging appearance. CONCLUSION. Desmoids are locally aggressive fibrous tumors with a tendency to recur. Desmoids can be intraabdominal, in the abdominal wall, or extraabdominal. Complications, such as compression or invasion of adjacent structures, and abscess formation can occur. Treatment options include observation, local treatment (surgery, radiotherapy), or systemic therapy (conventional chemotherapy, molecular targeted agents).
引用
收藏
页码:W1008 / W1014
页数:7
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