Fenestration of extracardiac Fontan and reversal of protein-losing enteropathy: Case report

被引:14
作者
Lemes, V
Murphy, AM
Osterman, FA
Laschinger, JC
Kan, JS
机构
[1] Johns Hopkins Hosp, Dept Pediat, Div Pediat Cardiol, Baltimore, MD 21287 USA
[2] Johns Hopkins Hosp, Dept Radiol, Baltimore, MD 21287 USA
[3] Johns Hopkins Hosp, Dept Cardiothorac Surg, Baltimore, MD 21287 USA
关键词
Fontan operation; protein-losing enteropathy;
D O I
10.1007/s002469900322
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
We describe a patient with protein-losing enteropathy who presented 6 months after undergoing a modified Fontan operation. After failing to respond to medical therapy, the Fontan tunnel was fenestrated by catheter intervention with immediate improvement and resolution of hypoproteinemia and enteric protein loss.
引用
收藏
页码:355 / 357
页数:3
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