Single-Ventricle Palliation in a 4-Year-Old With Ehlers-Danlos Syndrome

被引：0

作者：

DeBoard, Zach M.

Eckhauser, Aaron W.

Griffiths, Eric

机构：

[1] Univ Utah, Div Cardiothorac Surg, Salt Lake City, UT 84103 USA

[2] Primary Childrens Med Ctr, Pediat Cardiothorac Surg, Salt Lake City, UT 84103 USA

来源：

ANNALS OF THORACIC SURGERY | 2018年 / 105卷 / 01期

关键词：

LEFT-HEART SYNDROME; DILATION;

D O I：

10.1016/j.athoracsur.2017.08.027

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

We report the case of a 4-year-old boy with Ehlers-Danlos syndrome undergoing single-ventricle palliation for an unbalanced atrioventricular canal defect. No reports of single-ventricle palliation in the setting of connective tissue disorders exist in the current literature. Unique findings on the patient's preoperative imaging included a disproportionately large neoaortic root and a regurgitant atrioventricular valve, which may foretell the need for future intervention. (C) 2018 by The Society of Thoracic Surgeons

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收藏

页码：E31 / E32

页数：2

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