Long-term outcomes in 3 cases of quadricuspid aortic valve, using a new classification system: A case series and literature review

被引:6
作者
Tsugu, Toshimitsu [1 ]
Murata, Mitsushige [2 ]
Endo, Jin [1 ]
Kawakami, Takashi [1 ]
Tsuruta, Hikaru [1 ]
Itabashi, Yuji [1 ]
Fukuda, Keiichi [1 ]
机构
[1] Keio Univ, Dept Cardiol, Sch Med, Tokyo, Japan
[2] Keio Univ, Ctr Prevent Med, Sch Med, Tokyo, Japan
来源
ECHOCARDIOGRAPHY-A JOURNAL OF CARDIOVASCULAR ULTRASOUND AND ALLIED TECHNIQUES | 2019年 / 36卷 / 03期
关键词
aortic insufficiency; aortic regurgitation; aortic valve; congenital heart disease; echocardiography;
D O I
10.1111/echo.14278
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Quadricuspid aortic valve has been classified based on leaflet size. However, no association is seen between classification and severity of aortic regurgitation (AR). Bicuspid aortic valve is classified according to the number of cusps, with significantly higher prevalence of AR in cases with a raphe. We classified cases according to raphe number. In 1 patient with no raphe, AR severity did not change into the eighth decade. However, AR severity worsened in patients with a raphe, in 1 case requiring aortic valve replacement in the fifth decade. Unequal shear stress may lead to leaflet fibrosis and progressive AR.
引用
收藏
页码:595 / 597
页数:3
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