Management of Unoperated Tetralogy of Fallot in a 59-Year-Old Patient

被引:5
作者
Boyer, Robin [1 ,2 ]
Kim, Hyung Jin [1 ,2 ]
Krishnan, Rajagopal [1 ,2 ]
机构
[1] Riverside Univ Hlth Syst, Moreno Valley, CA USA
[2] Loma Linda Univ, Med Ctr, Loma Linda, CA USA
关键词
tetralogy of Fallot; management; unoperated; unrepaired; REPAIR; AGE;
D O I
10.1177/2324709620926908
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Tetralogy of Fallot is the most common cyanotic congenital heart defect consisting of an overriding aorta, right ventricular outflow obstruction, ventricular septal defect, and right ventricular hypertrophy. Without surgical management, approximately only 3% of patients survive past the age of 40 years. Cases of unoperated patients reaching adulthood have been reported; however, few studies describe treatment guidelines for surgical or therapeutic management. In this article, we report the case of a 59-year-old Hispanic male with unoperated tetralogy of Fallot presenting to our cardiology clinic for initial workup and management.
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页数:3
相关论文
共 11 条
[1]   LIFE EXPECTANCY WITHOUT SURGERY IN TETRALOGY OF FALLOT [J].
BERTRANOU, EG ;
BLACKSTONE, EH ;
HAZELRIG, JB ;
TURNER, ME ;
KIRKLIN, JW .
AMERICAN JOURNAL OF CARDIOLOGY, 1978, 42 (03) :458-466
[2]   THE SURGICAL-TREATMENT OF MALFORMATIONS OF THE HEART - IN WHICH THERE IS PULMONARY STENOSIS OR PULMONARY ATRESIA (REPRINTED) [J].
BLALOCK, A ;
TAUSSIG, HB .
JAMA-JOURNAL OF THE AMERICAN MEDICAL ASSOCIATION, 1984, 251 (16) :2123-2138
[3]  
Centers for Disease Control and Prevention, CONG HEART DEF FACTS
[4]   TOTAL CORRECTION OF TETRALOGY OF FALLOT AT AGE 40 YEARS AND OLDER - LONG-TERM FOLLOW-UP [J].
HU, DCK ;
SEWARD, JB ;
PUGA, FJ ;
FUSTER, V ;
TAJIK, AJ .
JOURNAL OF THE AMERICAN COLLEGE OF CARDIOLOGY, 1985, 5 (01) :40-44
[5]   Tetralogy of Fallot Repair in Patients 40 Years or Older [J].
Jost, Christine H. Attenhofer ;
Connolly, Heidi M. ;
Burkhart, Harold M. ;
Scott, Christopher G. ;
Dearani, Joseph A. ;
Carroll, Aisling J. ;
Tajik, A. Jamil .
MAYO CLINIC PROCEEDINGS, 2010, 85 (12) :1090-1094
[6]   LONG-TERM OUTCOME IN PATIENTS UNDERGOING SURGICAL REPAIR OF TETRALOGY OF FALLOT [J].
MURPHY, JG ;
GERSH, BJ ;
MAIR, DD ;
FUSTER, V ;
MCGOON, MD ;
ILSTRUP, DM ;
MCGOON, DC ;
KIRKLIN, JW ;
DANIELSON, GK .
NEW ENGLAND JOURNAL OF MEDICINE, 1993, 329 (09) :593-599
[7]  
Prakash SS., 2014, BMJ CASE REP, V2014
[8]   Survival to the age of 87 years in a woman with unoperated tetralogy of Fallot [J].
Subhawong, Ty K. ;
Teytelboym, Oleg .
JOURNAL OF RADIOLOGY CASE REPORTS, 2009, 3 (08) :14-17
[9]  
Van Arsdell GS, 2000, CIRCULATION, V102, P123
[10]   Unoperated tetralogy of Fallot: case report of a natural survivor who died in his 73rd year; is it ever too late to operate? [J].
Yang, X ;
Freeman, LJ ;
Ross, C .
POSTGRADUATE MEDICAL JOURNAL, 2005, 81 (952) :133-134