Cardiac manifestations in tuberous sclerosis: A 10-year review

被引：13
作者：
Quek, SC
Yip, W
Quek, ST
Chang, SK
Wong, ML
Low, PS
机构：
[1] Natl Univ Singapore, Dept Paediat, Singapore 117548, Singapore
[2] Natl Univ Singapore Hosp, Dept Diagnost Imaging, Singapore 117548, Singapore
来源：
JOURNAL OF PAEDIATRICS AND CHILD HEALTH | 1998年 / 34卷 / 03期
基金：
美国国家卫生研究院;
关键词：
cardiac tumour; rhabdomyoma; seizures; tuberous sclerosis;
D O I：
10.1046/j.1440-1754.1998.00218.x
中图分类号：
R72 [儿科学];
学科分类号：
100202 ;
摘要：
Objective: Tuberous sclerosis is a genetic disorder with multisystem involvement. The aim of this study was to focus primarily on the cardiac aspects of this condition. Method: This review included 10 children with tuberous sclerosis presenting to our department during a 10-year period. Results: From our data, 80% were found to have cardiac involvement. There was an equal prevalence of neurologic complications. Conclusions: Cardiac tumours and seizures were the most common problems encountered. Whereas most patients had no symptoms referable to the cardiovascular system and required no active intervention, many of those with neurologic involvement needed appropriate treatment.
引用
收藏
页码：283 / 287
页数：5
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