Investigation and Management of Erythrocytosis

被引：31

作者：

McMullin, Mary Frances ^{[1
]}

机构：

[1] Queens Univ Belfast, Belfast City Hosp, Haematol, C Floor,Lisburn Rd, Belfast BT9 7AB, Antrim, North Ireland

来源：

CURRENT HEMATOLOGIC MALIGNANCY REPORTS | 2016年 / 11卷 / 05期

关键词：

Erythrocytosis; Myeloproliferative disorders; Management; Treatment; CONGENITAL ERYTHROCYTOSIS; MISSENSE MUTATION; POLYCYTHEMIA; DIAGNOSIS; ADULTS; BLOOD;

D O I：

10.1007/s11899-016-0334-1

中图分类号：

R73 [肿瘤学];

学科分类号：

100214 ;

摘要：

An absolute erythrocytosis is present when the red cell mass is greater than 125 % of the predicted value for sex and body mass. It can have a primary or secondary and congenital or acquired cause. New causes particularly congenital continue to be discovered and investigated. Investigation for the cause starts with repeat and confirmation of the raised hemoglobin and measurement of an erythropoietin level to indicate whether to pursue primary or secondary causes and then further investigations as appropriate. Management options include low dose aspirin and venesection. Specific management advice is available for certain specific clinical situations.

引用

收藏

页码：342 / 347

页数：6

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