End-stage renal disease in a patient with congenital lymphangiectasia and lymphedema

被引：5

作者：

Sombolos, KI ^{[1
]}

Papachillea, AI ^{[1
]}

Natse, TM ^{[1
]}

Gogos, KI ^{[1
]}

Pavlidis, GO ^{[1
]}

Barboutis, KA ^{[1
]}

Mavromatidis, KS ^{[1
]}

机构：

[1] Renal Unit GH G Papanikolaou, Thessaloniki, Greece

来源：

PEDIATRIC NEPHROLOGY | 2001年 / 16卷 / 02期

关键词：

end-stage renal disease; hemodialysis; lymphangiectasia; lymphedema;

D O I：

10.1007/s004670000526

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

Congenital lymphangiectasia with lymphedema is a disorder constituting the main defect in many different genetic syndromes. Herein we describe a 23-year-old male patient with congenital lymphangiectasia and severe lymphedema of the right leg, scrotum, and abdominal wall, who presented with end-stage renal disease, presumably due to cystic renal lymphangiectasia, and is undergoing chronic hemodialysis treatment.

引用

页码：151 / 153

页数：3

共 8 条

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