Brain histopathology in three cases of Susac's syndrome: implications for lesion pathogenesis and treatment

被引:49
作者
Hardy, Todd A. [1 ,2 ,3 ]
O'Brien, Billy [4 ]
Gerbis, Natasha [5 ]
Barnett, Michael H. [3 ,6 ,7 ]
Reddel, Stephen W. [1 ,2 ]
Brewer, Janice [8 ]
Herkes, Geoffrey K. [5 ]
Silberstein, Paul [5 ]
Garsia, Roger J. [9 ]
Watson, John D. G. [10 ,11 ]
Gupta, Ruta [2 ,12 ]
Parratt, John D. E. [5 ,13 ]
Buckland, Michael E. [6 ,14 ]
机构
[1] Concord Hosp, Neuroimmunol Clin, Sydney, NSW, Australia
[2] Univ Sydney, Sydney, NSW 2006, Australia
[3] Brain & Mind Res Inst, MS Australia Clin, Sydney, NSW, Australia
[4] Gosford Hosp, Dept Neurol, Gosford, Australia
[5] Royal N Shore Hosp, Dept Neurol, Sydney, NSW, Australia
[6] Brain & Mind Res Inst, Sydney, NSW, Australia
[7] Royal Prince Alfred Hosp, Dept Neurol, Sydney, NSW, Australia
[8] Royal N Shore Hosp, PaLMS, Dept Anat Pathol, Sydney, NSW, Australia
[9] Royal Prince Alfred Hosp, Dept Immunol, Sydney, NSW, Australia
[10] Sydney Adventist Hosp, Neurol Sect, Sydney, NSW, Australia
[11] Univ Sydney, Discipline Med, Sydney Adventist Hosp Clin Sch, Sydney, NSW 2006, Australia
[12] Royal Prince Alfred Hosp, Dept Tissue Pathol & Diagnost Oncol, Sydney, NSW, Australia
[13] Univ Sydney, Dept Med, Inst Clin Neurosci, Camperdown, NSW, Australia
[14] Royal Prince Alfred Hosp, Dept Neuropathol, Sydney, NSW, Australia
关键词
RETINAL ARTERIOLAR OCCLUSIONS; HEARING-LOSS; ENCEPHALOPATHY;
D O I
10.1136/jnnp-2014-308240
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
引用
收藏
页码:582 / +
页数:3
相关论文
共 7 条
  • [1] Treatment of Susac syndrome with gamma globulin and corticosteroids
    Fox, Robert J.
    Costello, Fiona
    Judkins, Alexander R.
    Galetta, Steven L.
    Maguire, Albert M.
    Leonard, Brian
    Markowitz, Clyde E.
    [J]. JOURNAL OF THE NEUROLOGICAL SCIENCES, 2006, 251 (1-2) : 17 - 22
  • [2] Tumour necrosis factor (TNF) inhibitor therapy in Susac's syndrome
    Hardy, T. A.
    Garsia, R. J.
    Halmagyi, G. M.
    Lewis, S. J. G.
    Harrisberg, B.
    Fulham, M. J.
    Barnett, M. H.
    [J]. JOURNAL OF THE NEUROLOGICAL SCIENCES, 2011, 302 (1-2) : 126 - 128
  • [3] MICROANGIOPATHY WITH ENCEPHALOPATHY, HEARING-LOSS AND RETINAL ARTERIOLAR OCCLUSIONS - 2 NEW CASES
    HEISKALA, H
    SOMER, H
    KOVANEN, J
    POUTIAINEN, E
    KARLI, H
    HALTIA, M
    [J]. JOURNAL OF THE NEUROLOGICAL SCIENCES, 1988, 86 (2-3) : 239 - 250
  • [4] Susac Syndrome An Organ-Specific Autoimmune Endotheliopathy Syndrome Associated With Anti-Endothelial Cell Antibodies
    Magro, Cynthia M.
    Poe, Jonathan C.
    Lubow, Martin
    Susac, John O.
    [J]. AMERICAN JOURNAL OF CLINICAL PATHOLOGY, 2011, 136 (06) : 903 - 912
  • [5] A MICRO-ANGIOPATHIC SYNDROME OF ENCEPHALOPATHY, HEARING-LOSS, AND RETINAL ARTERIOLAR OCCLUSIONS
    MONTEIRO, MLR
    SWANSON, RA
    COPPETO, JR
    CUNEO, RA
    DEARMOND, SJ
    PRUSINER, SB
    [J]. NEUROLOGY, 1985, 35 (08) : 1113 - 1121
  • [6] Smolen JS, 2011, ARTHRITIS RES THER, V13, DOI [10.1186/1478-6354-13-S1-S2, 10.1186/ar3094]
  • [7] MRI findings in Susac's syndrome
    Susac, JO
    Murtagh, FR
    Egan, RA
    Berger, JR
    Bakshi, R
    Lincoff, N
    Gean, AD
    Galetta, SL
    Fox, RJ
    Costello, FE
    Lee, AG
    Clark, J
    Layzer, RB
    Daroff, RB
    [J]. NEUROLOGY, 2003, 61 (12) : 1783 - 1787