Therapeuticall approach of obesity in Prader-Willi syndrome

被引：3

作者：

De Carvalho, Daniel F. ^{[1
]}

Cercato, Cintia ^{[1
]}

Almeida, Madson Q. ^{[1
]}

Mancini, Marcio C. ^{[1
]}

Halpern, Alfredo ^{[1
]}

机构：

[1] Univ Sao Paulo, Fac Med, Grp Obesidade & Sindrome Met, Div Endocrinol,Hosp Clin, BR-05508 Sao Paulo, Brazil

来源：

ARQUIVOS BRASILEIROS DE ENDOCRINOLOGIA E METABOLOGIA | 2007年 / 51卷 / 06期

关键词：

obesity; Prader-Willi syndrome; pharmacological treatment; bariatric surgery; topiramate;

D O I：

10.1590/S0004-27302007000600004

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

Prader-Willi Syndrome (PWS) is a multisystemic genetic disease characterized by hypotonia, mental retardation, characteristic facial appearance, hyperphagia, and compulsive eating due to hypothalamic dysfunction. PWS is caused by loss of function of genes located in chromosome 15q11-q13, an area subject to genomic imprinting. Obesity is a major cause of increased morbidity and mortality among patients with PWS. The objective of this study was to analyze the therapeutic options available for the treatment of the obesity in PWS including pharmacological and surgical strategies.

引用

页码：913 / 919

页数：7

共 50 条

[21] Prader-Willi syndrome
Couper, RTL
JOURNAL OF PAEDIATRICS AND CHILD HEALTH, 1999, 35 (04) : 331 - 334
[22] Prader-Willi syndrome
Cassidy, Suzanne B.
Driscoll, Daniel J.
EUROPEAN JOURNAL OF HUMAN GENETICS, 2009, 17 (01) : 3 - 13
[23] Prader-Willi syndrome
Cassidy, SB
JOURNAL OF MEDICAL GENETICS, 1997, 34 (11) : 917 - 923
[24] Prader-Willi syndrome
Kundert, Deborah King
SCHOOL PSYCHOLOGY QUARTERLY, 2008, 23 (02) : 246 - 257
[25] Biliopancreatic diversion in Prader-Willi syndrome associated with obesity
Antal, SC
Levin, H
OBESITY SURGERY, 1996, 6 (01) : 58 - 62
[26] Prader-Willi Syndrome: Obesity due to Genomic Imprinting
Butler, Merlin G.
CURRENT GENOMICS, 2011, 12 (03) : 204 - 215
[27] Cross-cultural comparisons of obesity and growth in Prader-Willi syndrome
Dudley, O.
McManus, B.
Vogels, A.
Whittington, J.
Muscatelli, F.
JOURNAL OF INTELLECTUAL DISABILITY RESEARCH, 2008, 52 : 426 - 436
[28] Obesity treatment with liraglutide in a patient with Prader-Willi syndrome: a case report
Andres Cadena-Obando, Diego
Antonio Molina-Ayala, Mario
Ferreira-Hermosillo, Aldo
NUTRICION HOSPITALARIA, 2018, 35 (03) : 743 - 746
[29] Nutritional phases of Prader-Willi syndrome
Bravo, Paulina J.
Perez, Diego P.
Canals Cifuentes, Andrea
ANDES PEDIATRICA, 2021, 92 (03): : 359 - 366
[30] Gastric bypass in a Japanese man with Prader-Willi syndrome and morbid obesity
Kobayashi, J
Kodama, M
Yamazaki, K
Morikawa, O
Murano, S
Kawamata, N
Kawamura, I
OBESITY SURGERY, 2003, 13 (05) : 803 - 805

← 1 2 3 4 5 →