[1] Goethe Univ Frankfurt, Univ Hosp Frankfurt, Angioedema Ctr, Dept Children & Adolescents, D-60054 Frankfurt, Germany
[2] Charite, Dept Dermatol & Allergy, D-13353 Berlin, Germany
[3] Haemophilia Ctr Rhine Main, Morfelden Walldorf, Germany
[4] Barts Hlth NHS Trust, Dept Immunol, London, England
[5] Tech Univ Munich, Dept Otorhinolaryngol Head & Neck Surg, D-80290 Munich, Germany
[6] CREAK, Natl Reference Ctr Angioedema, Angers, France
[7] Hosp La Paz, Inst Hlth Res IdiPaz, Dept Allergy, Biomed Res Network Rare Dis CIBERER U754, Madrid, Spain
[8] Johannes Gutenberg Univ Mainz, Univ Med Ctr, Dept Dermatol, D-55122 Mainz, Germany
[9] Shire, Zug, Switzerland