B-cell lymphoma in a patient with WHIM syndrome

被引：41

作者：

Chae, KM ^{[1
]}

Ertle, JO ^{[1
]}

Tharp, MD ^{[1
]}

机构：

[1] Rush Presbyterian St Lukes Med Ctr, Dept Dermatol, Chicago, IL 60612 USA

来源：

JOURNAL OF THE AMERICAN ACADEMY OF DERMATOLOGY | 2001年 / 44卷 / 01期

关键词：

D O I：

10.1067/mjd.2001.111337

中图分类号：

R75 [皮肤病学与性病学];

学科分类号：

100206 ;

摘要：

WHIM syndrome is a rare congenital familial syndrome consisting of warts, hypogammaglobulinemia, infections, and myelokathexis. We describe a 30-year-old man with WHIM syndrome, in whom red dermal facial nodules developed. The diagnosis of B-cell lymphoma was established with biopsy and immunohistochemical studies. To our knowledge, this is the first reported case of WHIM syndrome complicated by a B-cell lymphoma.

引用

页码：124 / 128

页数：5

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