Anomalous origin of the left coronary artery from the pulmonary artery: A surgical certainty

被引：1

作者：

Butt, Ayesha ^{[1
]}

Amanullah, Muhammad Muneer ^{[2
]}

Ahmed, Mehnaz Atiq ^{[3
]}

Hasan, Asif ^{[4
]}

Ahmad, Waris ^{[5
]}

机构：

[1] Aga Khan Univ, Med Coll, Karachi, Pakistan

[2] Natl Inst Cardiovasc Dis, Dept Pediat Cardiac Serv, Karachi, Pakistan

[3] Liaquat Natl Hosp & Med Coll, Dept Pediat, Karachi, Pakistan

[4] Freeman Rd Hosp, Dept Cardio Thorac Surg, Newcastle, England

[5] Aga Khan Univ Hosp, Dept Surg, Karachi, Pakistan

来源：

JOURNAL OF THE PAKISTAN MEDICAL ASSOCIATION | 2020年 / 70卷 / 03期

关键词：

Bland-White-Garland syndrome; ALCAPA; Cardiovascular Diseases; Congenital Heart Defects; Coronary Vessel Anomalies; DIAGNOSIS; REPAIR;

D O I：

10.5455/JPMA.34200

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

This study aims to assess the clinical presentation and the outcomes of a surgical correction of an anomalous origin of the left coronary artery from the pulmonary artery (ALCAPA). A retrospective review was carried out on the charts of six patients admitted for ALCAPA surgery at Aga Khan University Hospital, Karachi from March 2017 to May 2018.Dyspnoea, palpitation, poor feeding, fatiguability, pallor and a murmur of mitral regurgitation were the main presenting features. The pre-operative median left ventricular ejection fraction (LVEF) was 64%. Coronary re-implantation was performed in all the patients with a mitral valve repair being done in only one patient. The mean LVEF was 66.3%, post-operatively. Mitral regurgitation (MR) improved in patients post-operatively with trace in 2 patients and mild MR in one. Surgical correction by coronary re-implantation yields favourable outcomes in ALCAPA and significantly reduces the morbidity and mortality rates associated with the disease.

引用

页码：561 / 564

页数：4

共 8 条

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