Macrophage Activation Syndrome: A Potentially Fatal Complication of Kawasaki Disease

被引:4
作者
Bose, Kallol [1 ]
Saha, Sudip [1 ]
Saha, Prabir [1 ]
Mondal, Piyasi [1 ]
机构
[1] Chittaranjan Seva Sadan Hosp, Dept Pediat, Kolkata 700026, W Bengal, India
关键词
Immunoglobulin; Kawasaki disease; macrophage activation syndrome;
D O I
10.5606/ArchRheumatol.2015.5186
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Kawasaki disease is an acute vasculitis of childhood. Macrophage activation syndrome is a rare life threatening complication. In this article, we report a five-year-six-month old girl patient with Kawasaki disease who developed irritability, hepatosplenomegaly, and pancytopenia after treatment with intravenous immunoglobulins. Patient's blood test and bone marrow aspiration results suggested macrophage activation syndrome. The patient responded to dexamethasone in a dose of 10 mg/m(2)/day.
引用
收藏
页码:178 / 180
页数:3
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