Macrophage Activation Syndrome: A Potentially Fatal Complication of Kawasaki Disease

被引：4

作者：

Bose, Kallol ^{[1
]}

Saha, Sudip ^{[1
]}

Saha, Prabir ^{[1
]}

Mondal, Piyasi ^{[1
]}

机构：

[1] Chittaranjan Seva Sadan Hosp, Dept Pediat, Kolkata 700026, W Bengal, India

来源：

ARCHIVES OF RHEUMATOLOGY | 2015年 / 30卷 / 02期

关键词：

Immunoglobulin; Kawasaki disease; macrophage activation syndrome;

D O I：

10.5606/ArchRheumatol.2015.5186

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

Kawasaki disease is an acute vasculitis of childhood. Macrophage activation syndrome is a rare life threatening complication. In this article, we report a five-year-six-month old girl patient with Kawasaki disease who developed irritability, hepatosplenomegaly, and pancytopenia after treatment with intravenous immunoglobulins. Patient's blood test and bone marrow aspiration results suggested macrophage activation syndrome. The patient responded to dexamethasone in a dose of 10 mg/m(2)/day.

引用

页码：178 / 180

页数：3

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