Isolated right subclavian artery arising from the right pulmonary artery via a right-sided ductus arteriosus with associated pulmonary steal phenomenon

被引:5
作者
Miller, Stephen G. [1 ]
Campbell, Michael J. [1 ]
Barker, Piers C. A. [1 ]
Hill, Kevin D. [1 ]
机构
[1] Duke Univ, Dept Pediat, Div Pediat Cardiol, Med Ctr, Durham, NC 27710 USA
关键词
Arch anomalies; DiGeorge syndrome; subclavian steal; RIGHT AORTIC-ARCH;
D O I
10.1017/S1047951111001065
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
We present a patient with DiGeorge syndrome and an isolated right subclavian artery arising from the right pulmonary artery via a right-sided ductus arteriosus. The patient showed a subclavian and pulmonary steal with perfusion of the right arm and right lung via retrograde circulation in the right vertebral artery. The patient underwent successful surgical repair.
引用
收藏
页码:216 / 218
页数:3
相关论文
共 11 条
[1]   ISOLATION OF THE RIGHT SUBCLAVIAN ARTERY WITH SUBCLAVIAN STEAL IN A CHILD WITH KLIPPEL-FEIL ANOMALY AN EXAMPLE OF THE SUBCLAVIAN ARTERY SUPPLY DISRUPTION SEQUENCE [J].
BRILL, CB ;
PEYSTER, RG ;
KELLER, MS ;
GALTMAN, L .
AMERICAN JOURNAL OF MEDICAL GENETICS, 1987, 26 (04) :933-940
[2]  
EDWARDS JE, 1948, MED CLIN N AM, P925
[3]   LEFT AORTIC-ARCH WITH CONGENITAL ISOLATION OF THE RIGHT SUBCLAVIAN ARTERY [J].
GARTI, IJ ;
AYGEN, MM .
PEDIATRIC RADIOLOGY, 1980, 9 (04) :241-243
[4]   SYMPTOMATOLOGY OF SUBCLAVIAN STEAL SYNDROME [J].
HEIDRICH, H ;
BAYER, O .
ANGIOLOGY, 1969, 20 (07) :406-&
[5]  
Jones TK, 1999, CATHETER CARDIO INTE, V47, P320, DOI 10.1002/(SICI)1522-726X(199907)47:3<320::AID-CCD15>3.0.CO
[6]  
2-V
[7]   SELECTIVE CYANOSIS OF THE RIGHT ARM - ISOLATION OF RIGHT SUBCLAVIAN ARTERY FROM AORTA WITH BILATERAL DUCTUS-ARTERIOSUS AND PULMONARY-HYPERTENSION [J].
KEAGY, KS ;
SCHALL, SA ;
HERRINGTON, RT .
PEDIATRIC CARDIOLOGY, 1982, 3 (04) :301-303
[8]   RIGHT AORTIC-ARCH WITH ISOLATION OF THE LEFT SUBCLAVIAN ARTERY - CASE-REPORT AND REVIEW OF THE LITERATURE [J].
LUETMER, PH ;
MILLER, GM .
MAYO CLINIC PROCEEDINGS, 1990, 65 (03) :407-413
[9]   Isolation of the subclavian artery associated with chromosome 22q11 deletion [J].
Momma, K .
CARDIOLOGY IN THE YOUNG, 1999, 9 (02) :233-233
[10]   ISOLATION OF THE RIGHT SUBCLAVIAN ARTERY [J].
NATH, H .
AMERICAN JOURNAL OF ROENTGENOLOGY, 1989, 152 (02) :430-431