Vein of Galen Malformations: Epidemiology, Clinical Presentations, Management

被引:53
作者
Recinos, Pablo F. [1 ,2 ]
Rahmathulla, Gazanfar [2 ]
Pearl, Monica [3 ]
Recinos, Violette Renard
Jallo, George I. [1 ]
Gailloud, Philippe [3 ]
Ahn, Edward S. [1 ]
机构
[1] Johns Hopkins Univ Hosp, Div Pediat Neurosurg, Baltimore, MD 21287 USA
[2] Cleveland Clin, Dept Neurosurg, Rosa Ella Burkhardt Brain Tumor & Neurooncol Ctr, Cleveland, OH 44195 USA
[3] Johns Hopkins Univ Hosp, Div Intervent Neuroradiol, Baltimore, MD 21287 USA
关键词
Vein of galen malformation; Arteriovenous malformation; Clinical presentation; Management; SPIRAL COMPUTED-TOMOGRAPHY; ANEURYSMAL MALFORMATION; ARTERIOVENOUS-MALFORMATION; ENDOVASCULAR MANAGEMENT; VASCULAR MALFORMATIONS; VENOUS DRAINAGE; EMBOLIZATION; CHILDREN; DIAGNOSIS; FAILURE;
D O I
10.1016/j.nec.2011.09.006
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
The vein of Galen aneurysmal malformation is a congenital vascular malformation that comprises 30% of the pediatric vascular and 1% of all pediatric congenital anomalies. Treatment is dependent on the timing of presentation and clinical manifestations. With the development of endovascular techniques, treatment paradigms have changed and clinical outcomes have significantly improved. In this article, the developmental embryology, clinical features and pathophysiology, diagnostic workup, and management strategies are reviewed.
引用
收藏
页码:165 / +
页数:14
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