Wilms Tumor (Nephroblastoma), Version 2.2021

被引:16
|
作者
Balis, Frank [1 ]
Green, Daniel M. [2 ]
Anderson, Clarke [3 ]
Cook, Shelly [4 ]
Dhillon, Jasreman [5 ]
Gow, Kenneth [6 ]
Hiniker, Susan [7 ]
Jasty-Rao, Rama [8 ]
Lin, Chi [9 ]
Lovvorn, Harold, III [10 ]
MacEwan, Iain [11 ]
Martinez-Agosto, Julian [12 ]
Mullen, Elizabeth [13 ]
Murphy, Erin S. [14 ,15 ]
Ranalli, Mark [16 ,17 ]
Rhee, Daniel [18 ]
Rokitka, Denise [19 ]
Tracy, Elisabeth [20 ]
Vern-Gross, Tamara [21 ]
Walsh, Michael F. [22 ]
Walz, Amy [23 ]
Wickiser, Jonathan [24 ]
Zapala, Matthew [25 ]
Berardi, Ryan A. [26 ]
Hughes, Miranda [26 ]
机构
[1] Univ Penn, Abramson Canc Ctr, Philadelphia, PA 19104 USA
[2] Univ Tennessee, Ctr Hlth Sci, St Jude Childrens Res Hosp, Memphis, TN 38163 USA
[3] City Hope Natl Med Ctr, 1500 E Duarte Rd, Duarte, CA 91010 USA
[4] Univ Wisconsin, Carbone Canc Ctr, Madison, WI USA
[5] H Lee Moffitt Canc Ctr & Res Inst, Tampa, FL USA
[6] Fred Hutchinson Canc Res Ctr, Seattle Canc Care Alliance, 1124 Columbia St, Seattle, WA 98104 USA
[7] Stanford Canc Inst, Stanford, CA USA
[8] Univ Michigan, Rogel Canc Ctr, Ann Arbor, MI 48109 USA
[9] Fred & Pamela Buffett Canc Ctr, Omaha, NE USA
[10] Vanderbilt Ingram Canc Ctr, Nashville, TN USA
[11] UC San Diego Moores Canc Ctr, San Diego, CA USA
[12] UCLA Jonsson Comprehens Canc Ctr, Los Angeles, CA USA
[13] Dana Farber Brigham & Womens Canc Ctr, Boston, MA USA
[14] Univ Hosp, Seidman Canc Ctr, Case Comprehens Canc Ctr, Cleveland, OH USA
[15] Cleveland Clin, Taussig Canc Inst, Cleveland, OH 44106 USA
[16] Ohio State Univ, Comprehens Canc Ctr, James Canc Hosp, Columbus, OH 43210 USA
[17] Ohio State Univ, Solove Res Inst, Columbus, OH 43210 USA
[18] Sidney Kimmel Comprehens Canc Ctr Johns Hopkins, Baltimore, MD USA
[19] Roswell Park Comprehens Canc Ctr, Buffalo, NY USA
[20] Duke Canc Inst, Durham, NC USA
[21] Mayo Clin, Canc Ctr, Rochester, MN USA
[22] Mem Sloan Kettering Canc Ctr, 1275 York Ave, New York, NY 10021 USA
[23] Northeastern Univ, Robert H Lurie Comprehens Canc Ctr, Boston, MA 02115 USA
[24] UT Southwestern Simmons Comprehens Canc Ctr, Dallas, TX USA
[25] UCSF Helen Diller Family Comprehens Canc Ctr, San Francisco, CA USA
[26] Natl Comprehens Canc Network, Plymouth Meeting, PA USA
来源
JOURNAL OF THE NATIONAL COMPREHENSIVE CANCER NETWORK | 2021年 / 19卷 / 08期
关键词
CHILDRENS ONCOLOGY GROUP; BECKWITH-WIEDEMANN-SYNDROME; ADVERSE PROGNOSTIC-FACTOR; INTERNATIONAL-SOCIETY; PEDIATRIC-ONCOLOGY; RENAL TUMORS; RADIATION-THERAPY; CHILDHOOD-CANCER; ACTINOMYCIN-D; DIAGNOSTIC PERFORMANCE;
D O I
10.6004/jnccn.2021.0037
中图分类号
R73 [肿瘤学];
学科分类号
100214 ;
摘要
The NCCN Guidelines for Wilms Tumor focus on the screening, diagnosis, staging, treatment, and management of Wilms tumor (WT, also known as nephroblastoma). WT is the most common primary renal tumor in children. Five-year survival is more than 90% for children with all stages of favorable histology WT who receive appropriate treatment. All patients with WT should be managed by a multidisciplinary team with experience in managing renal tumors; consulting a pediatric oncologist is strongly encouraged. Treatment of WT includes surgery, neoadjuvant or adjuvant chemotherapy, and radiation therapy (RT) if needed. Careful use of available therapies is necessary to maximize cure and minimize long-term toxicities. This article discusses the NCCN Guidelines recommendations for favorable histology WT.
引用
收藏
页码:945 / 977
页数:33
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