Takayasu arteritis

被引:6
作者
Mirault, T. [1 ,2 ,3 ]
Messas, E. [1 ,2 ,3 ]
机构
[1] Univ Paris 05, Hop Univ Paris Ouest, Hop Europeen Georges Pompidou,AP HP, Pole Cardiovasc Renal & Metabol,Serv Med Vasc, 20 Rue Leblanc, F-75015 Paris, France
[2] Hop Europeen Georges Pompidou, Ctr Natl Reference Malad Vasc Rares, F-75015 Paris, France
[3] Univ Paris 05, Sorbonne Paris Cite, INSERM, U970,PARCC, F-75015 Paris, France
来源
REVUE DE MEDECINE INTERNE | 2016年 / 37卷 / 04期
关键词
Aortitis; Takayasu arteritis; LARGE-VESSEL VASCULITIS; DISEASE-ACTIVITY; CRITERIA; CLASSIFICATION; MULTICENTER; EXPERIENCE; MANAGEMENT;
D O I
10.1016/j.revmed.2015.12.024
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Takayasu arteritis is a chronic inflammatory vasculitis of unknown origin affecting large vessels, predominantly the aorta and its main branches. Vessel inflammation leads to wall thickening, fibrosis, and stenosis. The lesions are often asymptomatic leading to limb numbness, transient ischemic attack, cardiovascular event and renovascular hypertension. Treatment is based on corticosteroids, immunosuppressant and biologics if necessary. Endovascular treatment and open-surgery can be useful for end-organ ischemia relief. (C) 2016 Published by Elsevier Masson SAS on behalf of the Societe nationale francaise de medecine interne (SNFMI).
引用
收藏
页码:223 / 229
页数:7
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