Mediastinal lipoblastoma with intraspinal extension: MRI demonstration

被引:27
作者
Ko, SF [1 ]
Shieh, CS [1 ]
Shih, TY [1 ]
Hsiao, CC [1 ]
Ng, SH [1 ]
Lee, TY [1 ]
Wan, YL [1 ]
Chen, WJ [1 ]
机构
[1] Chang Gung Mem Hosp, Dept Radiol, Kaohsiung, Taiwan
关键词
children; neoplasms; mediastinum; spine; magnetic resonance imaging;
D O I
10.1016/S0730-725X(98)00015-0
中图分类号
R8 [特种医学]; R445 [影像诊断学];
学科分类号
1002 ; 100207 ; 1009 ;
摘要
Lipoblastomatous lesions are mesenchymal tumors of embryonal white fat and are classified into two forms: a superficial, well-defined mass (lipoblastoma) or a deep, infiltrative lesion (lipoblastomatosis), We report an unique case of mediastinal lipoblastoma in a 17-month-old boy which harbored a dual nature and exhibited the characteristics of both forms, a large well-encapsulated intrathoracic main tumor.with focal infiltrative features at the thoracic inlet and transforaminal intraspinal extension forming a long-segment extradural mass. In addition to specific signal characterization of a fatty mediastinal mass with intratumoral streaks and whorls corresponding to the fibrovascular network, magnet ic resonance (MR) imaging offered clear demonstration of the chest wall, lower neck and intraspinal extension, which was important for preoperative planning. (C) 1998 Elsevier Science Inc.
引用
收藏
页码:445 / 448
页数:4
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