Fetal and Neonatal Presentation of Long QT Syndrome

被引：13

作者：

Komarlu, Rukmini ^{[1
]}

Beerman, Lee ^{[1
]}

Freeman, David ^{[2
]}

Arora, Gaurav ^{[1
]}

机构：

[1] UPMC, Childrens Hosp Pittsburgh, Dept Pediat Cardiol, Pittsburgh, PA 15224 USA

[2] St Vincents Med Ctr, Dept Pediat Cardiol, Pittsburgh, PA USA

来源：

PACE-PACING AND CLINICAL ELECTROPHYSIOLOGY | 2012年 / 35卷 / 04期

关键词：

pediatrics; long QT; IMPLANTABLE CARDIOVERTER-DEFIBRILLATOR; ISOPROTERENOL; ARRHYTHMIA;

D O I：

10.1111/j.1540-8159.2011.03040.x

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

This report describes a fetus presenting with intrauterine tachycardia and hydrops fetalis. Soon after birth the neonate was noted to be in torsades de pointes that responded dramatically to medical management. Long QT syndrome (LQTS) was diagnosed on electrocardiogram obtained soon after birth. The prognosis is poor when LQTS presents in utero or during the first week of life. However, our infant did well with medical management and has remained free of arrhythmias at follow-up.

引用

页码：e77 / e80

页数：4

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