A diagnostic challenge in the management of unlocalised persistent hyperinsulinaemic hypoglycaemia of infancy: A case report and review of literature

被引：0
作者：
Chung, P. H. Y. [1 ]
Wong, K. K. Y. [1 ]
Tsot, N. S. [2 ]
Low, L. C. K. [2 ]
Khoo, U. S. [3 ]
Tam, P. K. H. [1 ]
机构：
[1] Univ Hong Kong, Queen Mary Hosp, Dept Paediat Surg, Hong Kong, Hong Kong, Peoples R China
[2] Univ Hong Kong, Queen Mary Hosp, Dept Paediat & Adolescent Med, Hong Kong, Hong Kong, Peoples R China
[3] Univ Hong Kong, Queen Mary Hosp, Dept Pathol, Hong Kong, Hong Kong, Peoples R China
来源：
HONG KONG JOURNAL OF PAEDIATRICS | 2008年 / 13卷 / 02期
关键词：
hyperinsulinism; hypoglycaemia; infant; management;
D O I：
暂无
中图分类号：
R72 [儿科学];
学科分类号：
100202 ;
摘要：
Persistent hyperinsulinaemic hypoglycaemia of infancy (PHHI) is an uncommon condition that leads to hypoglycaemia in newborn or infancy. The responsible lesion can be either focal or diffuse within the pancreas. Being a rare disease entity in our locality, we describe our experience in managing an infant with focal PHHI that could not be localised by pre-operative investigations. Furthermore, a review of the literature is discussed.
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页码：125 / 129
页数：5
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