Trigeminal nerve hypertrophy in chronic inflammatory demyelinating polyradiculoneuropathy

被引:26
|
作者
Guibord, N
Chalk, C
Wein, F
Richardson, J
Snipes, GJ
Del Carpio, R
机构
[1] McGill Univ, Dept Pathol, Montreal, PQ, Canada
[2] McGill Univ, Dept Neurol, Montreal, PQ, Canada
[3] McGill Univ, Dept Ophthalmol, Montreal, PQ, Canada
[4] McGill Univ, Dept Diagnost Radiol, Montreal, PQ, Canada
关键词
D O I
10.1212/WNL.51.5.1459
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
An unusual clinical manifestation of nerve hypertrophy in chronic inflammatory demyelinating polyradiculoneuropathy (CIDP) is described. A patient with a 13-year history of CIDP developed diplopia and proptosis. Imaging of the neuraxis showed marked bilateral trigeminal nerve hypertrophy and lumbosacral nerve root hypertrophy. Biopsy of the night infraorbital nerve revealed inflammatory infiltrates and extensive onion bulb formation, consistent with CIDP.
引用
收藏
页码:1459 / 1462
页数:4
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