Laparoscopic excision of symmetric uterine remnants in a patient with Mayer-Rokitansky-Kuster-Hauser syndrome

Mayer-Rokitansky-Kuster-Hauser (MRKH) syndrome is an infrequent developmental defect characterized by congenital absence of the vagina and uterus. Various anomalies of the mullerian system have been operated on by laparoscopy. We performed operative laparoscopy to remove symmetric uterine remnants and right ovarian endometrioma in a woman with MRKH syndrome who suffered from intractable lower abdominal pain. Both anomalous structures, which had true uterine vessels, were located on their respective pelvic sidewalls close to the ureters. We suggest that operative laparoscopy can be performed safely to treat these patients, but careful identification and dissection of the main blood supply, if necessary, are of substantial importance in order to avoid ureteral injury.