Background: Marfan Syndrome (MS) is a dominantly inherited connective tissue disorder with consequences on the strength and resilience of connective tissues that may predispose to Pelvic Organ Prolapse (POP). Literature lacks studies investigating POP surgery in patients affected by MS that might help surgical management decisions. Objective: The objective of this paper is to describe the surgical procedure of laparoscopic sacral hysteropexy (LSHP) in a 37 years old woman affected by MS with symptomatic POP. Materials and Methods and main outcome measures: We performed a nerve-sparing laparoscopic sacral hysteropexy without complications and looked for anatomical and subjective outcomes. The patient completed The Female Sexual Distress Scale (FSDS), Pelvic Floor Disability Index (PFDI-20), and Wexner questionnaires preoperatively and postoperatively. Results: The patient stated a complete resolution of all POP related symptoms and there was a total correction of the descensus. Furthermore, no perioperative and postoperative complications were noted. Conclusions: LSHP could be an effective and safe procedure for the treatment of POP in women affected by MS and this case report is the first to describe a reconstructive procedure in this category of patients. What is new? The literature lacks studies investigating POP surgery in women with MS, that might help surgeons, thus we present this case to describe surgical and functional outcomes in this patient category, underlying the higher risk of complications and relapses related to the weakness of connective tissue. This case report may represent the basis of future studies to confirm the safety, efficacy and feasibility of LSHP and sacral colpopexy in patients with MS.
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[1]
[Anonymous], 1993, ENDOTHELIUM-J ENDOTH, DOI [10.3109/10623329309102697, DOI 10.3109/10623329309102697]
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Fdn Policlin Univ A Gemelli IRCCS, Dipartimento Sci Salute Donna & Bambino & Sanita, UOC Uroginecol & Chirurg Ricostrutt Pavimento Pel, Largo F Vito 1, I-00168 Rome, ItalyFdn Policlin Univ A Gemelli IRCCS, Dipartimento Sci Salute Donna & Bambino & Sanita, UOC Uroginecol & Chirurg Ricostrutt Pavimento Pel, Largo F Vito 1, I-00168 Rome, Italy
Campagna, Giuseppe
;
Vacca, Lorenzo
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Fdn Policlin Univ A Gemelli IRCCS, Dipartimento Sci Salute Donna & Bambino & Sanita, UOC Uroginecol & Chirurg Ricostrutt Pavimento Pel, Largo F Vito 1, I-00168 Rome, ItalyFdn Policlin Univ A Gemelli IRCCS, Dipartimento Sci Salute Donna & Bambino & Sanita, UOC Uroginecol & Chirurg Ricostrutt Pavimento Pel, Largo F Vito 1, I-00168 Rome, Italy
Vacca, Lorenzo
;
Panico, Giovanni
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Fdn Policlin Univ A Gemelli IRCCS, Dipartimento Sci Salute Donna & Bambino & Sanita, UOC Uroginecol & Chirurg Ricostrutt Pavimento Pel, Largo F Vito 1, I-00168 Rome, ItalyFdn Policlin Univ A Gemelli IRCCS, Dipartimento Sci Salute Donna & Bambino & Sanita, UOC Uroginecol & Chirurg Ricostrutt Pavimento Pel, Largo F Vito 1, I-00168 Rome, Italy
Panico, Giovanni
;
Rumolo, Valerio
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Fdn Policlin Univ A Gemelli IRCCS, Dipartimento Sci Salute Donna & Bambino & Sanita, UOC Uroginecol & Chirurg Ricostrutt Pavimento Pel, Largo F Vito 1, I-00168 Rome, ItalyFdn Policlin Univ A Gemelli IRCCS, Dipartimento Sci Salute Donna & Bambino & Sanita, UOC Uroginecol & Chirurg Ricostrutt Pavimento Pel, Largo F Vito 1, I-00168 Rome, Italy
Rumolo, Valerio
;
Caramazza, Daniela
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Fdn Policlin Univ A Gemelli IRCCS, Dipartimento Sci Salute Donna & Bambino & Sanita, UOC Uroginecol & Chirurg Ricostrutt Pavimento Pel, Largo F Vito 1, I-00168 Rome, ItalyFdn Policlin Univ A Gemelli IRCCS, Dipartimento Sci Salute Donna & Bambino & Sanita, UOC Uroginecol & Chirurg Ricostrutt Pavimento Pel, Largo F Vito 1, I-00168 Rome, Italy
Caramazza, Daniela
;
Lombisani, Andrea
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Fdn Policlin Univ A Gemelli IRCCS, Dipartimento Sci Salute Donna & Bambino & Sanita, UOC Uroginecol & Chirurg Ricostrutt Pavimento Pel, Largo F Vito 1, I-00168 Rome, ItalyFdn Policlin Univ A Gemelli IRCCS, Dipartimento Sci Salute Donna & Bambino & Sanita, UOC Uroginecol & Chirurg Ricostrutt Pavimento Pel, Largo F Vito 1, I-00168 Rome, Italy
Lombisani, Andrea
;
Rossitto, Cristiano
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Fdn Policlin Univ A Gemelli IRCCS, Dipartimento Sci Salute Donna & Bambino & Sanita, UOC Uroginecol & Chirurg Ricostrutt Pavimento Pel, Largo F Vito 1, I-00168 Rome, ItalyFdn Policlin Univ A Gemelli IRCCS, Dipartimento Sci Salute Donna & Bambino & Sanita, UOC Uroginecol & Chirurg Ricostrutt Pavimento Pel, Largo F Vito 1, I-00168 Rome, Italy
Rossitto, Cristiano
;
Gadonneix, Pierre
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Fdn St Jean de Dieu, Obstet & Gynaecol Dept, Paris, FranceFdn Policlin Univ A Gemelli IRCCS, Dipartimento Sci Salute Donna & Bambino & Sanita, UOC Uroginecol & Chirurg Ricostrutt Pavimento Pel, Largo F Vito 1, I-00168 Rome, Italy
Gadonneix, Pierre
;
Scambia, Giovanni
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Fdn Policlin Univ A Gemelli IRCCS, Dipartimento Sci Salute Donna & Bambino & Sanita, UOC Ginecol Oncol, Rome, Italy
Univ Cattolica Sacro Cuore, Ist Ginecol Ostetricia, Rome, ItalyFdn Policlin Univ A Gemelli IRCCS, Dipartimento Sci Salute Donna & Bambino & Sanita, UOC Uroginecol & Chirurg Ricostrutt Pavimento Pel, Largo F Vito 1, I-00168 Rome, Italy
机构:
Turgut Ozal Univ, Sch Med, Dept Obstet & Gynecol, TR-06560 Ankara, TurkeyTurgut Ozal Univ, Sch Med, Dept Obstet & Gynecol, TR-06560 Ankara, Turkey
Eser, Ayla
;
Unlubilgin, Eylem
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Etlik Zubeyde Hanim Training & Res Hosp, Dept Obstet & Gynecol, Ankara, TurkeyTurgut Ozal Univ, Sch Med, Dept Obstet & Gynecol, TR-06560 Ankara, Turkey
Unlubilgin, Eylem
;
Hizli, Fatih
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Dr Abdurrahman Yurtaslan Oncol Training & Res Hos, Dept Urol, Ankara, TurkeyTurgut Ozal Univ, Sch Med, Dept Obstet & Gynecol, TR-06560 Ankara, Turkey
Hizli, Fatih
;
Acar, Muradiye
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机构:
Turgut Ozal Univ, Sch Med, Dept Med Genet, TR-06560 Ankara, TurkeyTurgut Ozal Univ, Sch Med, Dept Obstet & Gynecol, TR-06560 Ankara, Turkey
机构:
Fdn Policlin Univ A Gemelli IRCCS, Dipartimento Sci Salute Donna & Bambino & Sanita, UOC Uroginecol & Chirurg Ricostrutt Pavimento Pel, Largo F Vito 1, I-00168 Rome, ItalyFdn Policlin Univ A Gemelli IRCCS, Dipartimento Sci Salute Donna & Bambino & Sanita, UOC Uroginecol & Chirurg Ricostrutt Pavimento Pel, Largo F Vito 1, I-00168 Rome, Italy
Campagna, Giuseppe
;
Vacca, Lorenzo
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Fdn Policlin Univ A Gemelli IRCCS, Dipartimento Sci Salute Donna & Bambino & Sanita, UOC Uroginecol & Chirurg Ricostrutt Pavimento Pel, Largo F Vito 1, I-00168 Rome, ItalyFdn Policlin Univ A Gemelli IRCCS, Dipartimento Sci Salute Donna & Bambino & Sanita, UOC Uroginecol & Chirurg Ricostrutt Pavimento Pel, Largo F Vito 1, I-00168 Rome, Italy
Vacca, Lorenzo
;
Panico, Giovanni
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Fdn Policlin Univ A Gemelli IRCCS, Dipartimento Sci Salute Donna & Bambino & Sanita, UOC Uroginecol & Chirurg Ricostrutt Pavimento Pel, Largo F Vito 1, I-00168 Rome, ItalyFdn Policlin Univ A Gemelli IRCCS, Dipartimento Sci Salute Donna & Bambino & Sanita, UOC Uroginecol & Chirurg Ricostrutt Pavimento Pel, Largo F Vito 1, I-00168 Rome, Italy
Panico, Giovanni
;
Rumolo, Valerio
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Fdn Policlin Univ A Gemelli IRCCS, Dipartimento Sci Salute Donna & Bambino & Sanita, UOC Uroginecol & Chirurg Ricostrutt Pavimento Pel, Largo F Vito 1, I-00168 Rome, ItalyFdn Policlin Univ A Gemelli IRCCS, Dipartimento Sci Salute Donna & Bambino & Sanita, UOC Uroginecol & Chirurg Ricostrutt Pavimento Pel, Largo F Vito 1, I-00168 Rome, Italy
Rumolo, Valerio
;
Caramazza, Daniela
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Fdn Policlin Univ A Gemelli IRCCS, Dipartimento Sci Salute Donna & Bambino & Sanita, UOC Uroginecol & Chirurg Ricostrutt Pavimento Pel, Largo F Vito 1, I-00168 Rome, ItalyFdn Policlin Univ A Gemelli IRCCS, Dipartimento Sci Salute Donna & Bambino & Sanita, UOC Uroginecol & Chirurg Ricostrutt Pavimento Pel, Largo F Vito 1, I-00168 Rome, Italy
Caramazza, Daniela
;
Lombisani, Andrea
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Fdn Policlin Univ A Gemelli IRCCS, Dipartimento Sci Salute Donna & Bambino & Sanita, UOC Uroginecol & Chirurg Ricostrutt Pavimento Pel, Largo F Vito 1, I-00168 Rome, ItalyFdn Policlin Univ A Gemelli IRCCS, Dipartimento Sci Salute Donna & Bambino & Sanita, UOC Uroginecol & Chirurg Ricostrutt Pavimento Pel, Largo F Vito 1, I-00168 Rome, Italy
Lombisani, Andrea
;
Rossitto, Cristiano
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机构:
Fdn Policlin Univ A Gemelli IRCCS, Dipartimento Sci Salute Donna & Bambino & Sanita, UOC Uroginecol & Chirurg Ricostrutt Pavimento Pel, Largo F Vito 1, I-00168 Rome, ItalyFdn Policlin Univ A Gemelli IRCCS, Dipartimento Sci Salute Donna & Bambino & Sanita, UOC Uroginecol & Chirurg Ricostrutt Pavimento Pel, Largo F Vito 1, I-00168 Rome, Italy
Rossitto, Cristiano
;
Gadonneix, Pierre
论文数: 0引用数: 0
h-index: 0
机构:
Fdn St Jean de Dieu, Obstet & Gynaecol Dept, Paris, FranceFdn Policlin Univ A Gemelli IRCCS, Dipartimento Sci Salute Donna & Bambino & Sanita, UOC Uroginecol & Chirurg Ricostrutt Pavimento Pel, Largo F Vito 1, I-00168 Rome, Italy
Gadonneix, Pierre
;
Scambia, Giovanni
论文数: 0引用数: 0
h-index: 0
机构:
Fdn Policlin Univ A Gemelli IRCCS, Dipartimento Sci Salute Donna & Bambino & Sanita, UOC Ginecol Oncol, Rome, Italy
Univ Cattolica Sacro Cuore, Ist Ginecol Ostetricia, Rome, ItalyFdn Policlin Univ A Gemelli IRCCS, Dipartimento Sci Salute Donna & Bambino & Sanita, UOC Uroginecol & Chirurg Ricostrutt Pavimento Pel, Largo F Vito 1, I-00168 Rome, Italy
机构:
Turgut Ozal Univ, Sch Med, Dept Obstet & Gynecol, TR-06560 Ankara, TurkeyTurgut Ozal Univ, Sch Med, Dept Obstet & Gynecol, TR-06560 Ankara, Turkey
Eser, Ayla
;
Unlubilgin, Eylem
论文数: 0引用数: 0
h-index: 0
机构:
Etlik Zubeyde Hanim Training & Res Hosp, Dept Obstet & Gynecol, Ankara, TurkeyTurgut Ozal Univ, Sch Med, Dept Obstet & Gynecol, TR-06560 Ankara, Turkey
Unlubilgin, Eylem
;
Hizli, Fatih
论文数: 0引用数: 0
h-index: 0
机构:
Dr Abdurrahman Yurtaslan Oncol Training & Res Hos, Dept Urol, Ankara, TurkeyTurgut Ozal Univ, Sch Med, Dept Obstet & Gynecol, TR-06560 Ankara, Turkey
Hizli, Fatih
;
Acar, Muradiye
论文数: 0引用数: 0
h-index: 0
机构:
Turgut Ozal Univ, Sch Med, Dept Med Genet, TR-06560 Ankara, TurkeyTurgut Ozal Univ, Sch Med, Dept Obstet & Gynecol, TR-06560 Ankara, Turkey