Dural ectasia in the Marfan syndrome: MR and CT findings and criteria

被引:69
作者
Ahn, NU
Sponseller, PD
Ahn, UM
Nallamshetty, L
Rose, PS
Buchowski, JM
Garrett, ES
Kuszyk, BS
Fishman, EK
Zinreich, SJ
机构
[1] Johns Hopkins Univ, Sch Med, Dept Radiol, Baltimore, MD 21205 USA
[2] Johns Hopkins Univ, Sch Med, Dept Oncol, Div Biostat, Baltimore, MD 21205 USA
[3] Johns Hopkins Univ, Sch Med, Dept Orthopaed Surg, Baltimore, MD 21205 USA
关键词
Marfan syndrome; connective tissue disease; dural ectasia; spinal deformity; diagnosis criteria;
D O I
10.1097/00125817-200005000-00003
中图分类号
Q3 [遗传学];
学科分类号
071007 ; 090102 ;
摘要
Purpose: To create criteria for detecting dural ectasia on MR or CT images in adult Marfan patients. Methods: Images were analyzed using a workstation. Parameters that predicted dural ectasia were included in our criteria. Results: Major criteria include: (1) width of dural sac below L5 > width above L4; (2) anterior sacral meningocele. Minor criteria include: (1) L5 nerve root sleeve diameter > 6.5 mm and (2) S1 scalloping > 3.5. Dural ectasia exists if 1 major or 2 minor criteria are present. Conclusion: MR and CT diagnose dural ectasia with high specificity and sensitivity. Our criteria accurately diagnose dural ectasia in adult Marfan patients.
引用
收藏
页码:173 / 179
页数:7
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