Absence of left pulmonary artery with the ipsilateral lung cancer and right aortic arch: a case report

被引:0
作者
Yang, Bo [1 ]
Cui, Yongsheng [1 ]
Yao, Jinhong [1 ]
Sun, Wei [1 ]
Li, Guanghu [1 ]
Shao, Guoguang [1 ]
机构
[1] Jilin Univ, Hosp 1, Dept Thorac Surg, 71 Xinmin St, Changchun 130021, Jilin, Peoples R China
关键词
Unilateral pulmonary agenesis/UAPA; lung cancer; aortic arch; pneumonectomy; CONGENITAL UNILATERAL ABSENCE; AGENESIS;
D O I
暂无
中图分类号
R-3 [医学研究方法]; R3 [基础医学];
学科分类号
1001 ;
摘要
Unilateral pulmonary agenesis is a medical condition characterized by the unilateral absence of pulmonary artery (UAPA). It is a rare congenital condition caused by malformation of pulmonary vascular system. Such patients often develop other congenital heart diseases, such as Tetralogy of Fallot, patent ductus arteriosus. In this report, we have described a 56-year-old male patient, who experienced an intermittent pain in the left side of the chest for two months. He also experienced persistent back pain. This patient was diagnosed with UAPA and ipsilateral lung cancer. This was an extremely rare case worldwide. After performing a contrast-enhanced lung CT, vascular imaging technology, bronchoscopy, and pathological examination are used to make a clear diagnosis of lung cancer, which was complicated by left pulmonary artery agenesis and a right aortic arch. The patient was treated with left lung resection. The postoperative recovery of the patient was good as he did not develop any complications. Therefore, the patient was discharged as his prognosis was positive.
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页码:14815 / 14820
页数:6
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