Skip segment Hirschsprung's disease: a rare phenomenon

被引：12

作者：

Doi, Takashi ^{[1
]}

O'Donnell, Anne-Marie ^{[1
]}

McDermott, Michael ^{[1
]}

Puri, Prem ^{[1
]}

机构：

[1] Our Ladys Hosp Sick Children, Childrens Res Ctr, Dublin 12, Ireland

来源：

PEDIATRIC SURGERY INTERNATIONAL | 2011年 / 27卷 / 07期

关键词：

Skip segment Hirschsprung's disease; Total colonic aganglionosis; AGANGLIONOSIS; AREA;

D O I：

10.1007/s00383-011-2903-7

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

Skip segment Hirschsprung's disease (SSHD) involves a skip area of normally ganglionated intestine, surrounded proximally and distally by aganglionosis. We report a case of SSHD in infant with total colonic aganglionosis (TCA). Although SSHD is a rare and controversial condition, it should be considered a definite entity in the evaluation of Hirschsprung's disease.

引用

页码：787 / 789

页数：3

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