Scrotum-perineal granular cell tumor in pediatric age: A case report

OBJECTIVE: Report a case of a scrotum-perineal Granular Cell Tumor (GCT) in pediatric age. METHODS: To report a case. RESULTS: A 12 years old men with a multiple GCT history, located in both extremities, abdomen and scrotumperineal region. Surgical excision of all lesions and a genetic study are performed to rule out Noonan syndrome. CONCLUSION: GCT or Abrikossoff tumor is a tumor with a very low incidence, especially in pediatric age. The most frequent form of presentation a solitary nodule and the most common behavior is in the form of a benign tumor. Immunohistochemistry is crucial for its diagnosis, the main characteristic is positivity for the S100 protein. Although scrotal location is very rare, it must be considered in the differential diagnosis of scrotal mass. Surgical excision is the treatment of choice.